G40.B01
BillableJuvenile myoclonic epilepsy, not intractable, with status epilepticus
HCC Category Mapping
What This Code Means
Juvenile myoclonic epilepsy (sudden involuntary muscle jerks, typically in adolescents) that responds to medication, currently experiencing status epilepticus.
Coding Tips
- •Juvenile myoclonic epilepsy typically begins in adolescence with myoclonic jerks upon waking
- •Status epilepticus in this condition may involve repeated myoclonic jerks or generalized tonic-clonic seizures
Clinical Significance
Juvenile myoclonic epilepsy (JME) with status epilepticus is a serious complication of this common adolescent-onset generalized epilepsy. JME is characterized by myoclonic jerks upon awakening, generalized tonic-clonic seizures, and sometimes absence seizures. Status epilepticus may involve myoclonic status or generalized convulsive status, both requiring emergency management.
Documentation Requirements
- ✓Confirmed JME diagnosis based on clinical history and EEG findings
- ✓Documentation of active status epilepticus during the encounter
- ✓Seizure types present (myoclonic, tonic-clonic, absence)
- ✓Statement that condition responds to medication (not intractable)
- ✓Emergency interventions provided
- ✓Typical triggers (sleep deprivation, alcohol, photic stimulation)