G40.814
BillableLennox-Gastaut syndrome, intractable, without status epilepticus
HCC Category Mapping
V28HCC 201 — Seizure Disorders and Convulsions
0.262V24HCC 79 — Seizure Disorders and Convulsions
0.244ESRDHCC 79 — Seizure Disorders and Convulsions
0.000RxHCCHCC 163 — Seizure Disorders, Intractable Epilepsy
0.000What This Code Means
Lennox-Gastaut syndrome, a severe childhood epilepsy with multiple seizure types that cannot be adequately controlled with medication, not currently in a prolonged seizure state.
Coding Tips
- •Document failed antiepileptic drug trials and consider noting if patient is evaluated for surgical options
- •This intractable form often requires multidisciplinary management including neurology and developmental pediatrics
Clinical Significance
Lennox-Gastaut syndrome, intractable, without status epilepticus is the most common clinical presentation of LGS — a severe epileptic encephalopathy that is typically drug-resistant. These patients have ongoing uncontrolled seizures despite multiple medication trials, significant cognitive impairment, and may be candidates for palliative epilepsy surgery, corpus callosotomy, or VNS therapy.
Documentation Requirements
- ✓Confirmed Lennox-Gastaut syndrome diagnosis with characteristic features
- ✓Documentation of intractability with list of failed antiepileptic drugs
- ✓Absence of status epilepticus at the encounter
- ✓Current seizure types and frequency
- ✓Cognitive and developmental status
- ✓Treatment plan including advanced therapy considerations
- ✓Multidisciplinary care team involvement
Commonly Confused Codes
G40.812 — LGS, NOT intractable; rare presentation where seizures are controlledG40.813 — LGS, intractable, WITH status epilepticusG40.824 — Epileptic spasms, intractable; distinct from LGS even though LGS may evolve from infantile spasmsG40.834 — Dravet syndrome, intractable; different epileptic encephalopathyG40.804 — Other epilepsy, intractable; less specific when LGS is confirmed
Code Hierarchy
└G40Epilepsy and recurrent seizures└G40.8Other epilepsy and recurrent seizures└G40.81Lennox-Gastaut syndrome└G40.814Lennox-Gastaut syndrome, intractable, without status epilepticus
└G40.814Lennox-Gastaut syndrome, intractable, without status epilepticus