G40.813
BillableLennox-Gastaut syndrome, intractable, with status epilepticus
HCC Category Mapping
V28HCC 201 — Seizure Disorders and Convulsions
0.262V24HCC 79 — Seizure Disorders and Convulsions
0.244ESRDHCC 79 — Seizure Disorders and Convulsions
0.000RxHCCHCC 163 — Seizure Disorders, Intractable Epilepsy
0.000What This Code Means
Lennox-Gastaut syndrome, a severe childhood epilepsy with multiple seizure types that cannot be adequately controlled with medication, currently experiencing a prolonged seizure state.
Coding Tips
- •Intractable Lennox-Gastaut is particularly challenging; document all medication trials and their outcomes
- •Status epilepticus in this intractable form is a medical emergency requiring intensive care
Clinical Significance
Lennox-Gastaut syndrome, intractable, with status epilepticus represents the most severe presentation of this already-serious epilepsy syndrome. Drug-resistant LGS with active status epilepticus is a medical emergency requiring intensive care. LGS is one of the most treatment-resistant epilepsy syndromes, and status epilepticus in this context may be prolonged and difficult to terminate.
Documentation Requirements
- ✓Confirmed Lennox-Gastaut syndrome diagnosis
- ✓Documentation of intractability with failed antiepileptic drug trials
- ✓Active status epilepticus during the encounter
- ✓Emergency interventions and ICU management
- ✓Complete medication history showing drug resistance
- ✓EEG and clinical features confirming LGS diagnosis
Commonly Confused Codes
G40.814 — LGS, intractable, WITHOUT status epilepticusG40.811 — LGS with status epilepticus but NOT intractableG40.803 — Other epilepsy, intractable, with status epilepticus; use when LGS is not confirmedG40.823 — Epileptic spasms, intractable, with status epilepticus; distinct conditionG40.833 — Dravet syndrome, intractable, with status epilepticus; different genetic epilepsy
Code Hierarchy
└G40Epilepsy and recurrent seizures└G40.8Other epilepsy and recurrent seizures└G40.81Lennox-Gastaut syndrome└G40.813Lennox-Gastaut syndrome, intractable, with status epilepticus
└G40.813Lennox-Gastaut syndrome, intractable, with status epilepticus