G40.811
BillableLennox-Gastaut syndrome, not intractable, with status epilepticus
HCC Category Mapping
V28HCC 201 — Seizure Disorders and Convulsions
0.262V24HCC 79 — Seizure Disorders and Convulsions
0.244ESRDHCC 79 — Seizure Disorders and Convulsions
0.000RxHCCHCC 164 — Seizure Disorders, Non-Intractable Epilepsy
0.000What This Code Means
Lennox-Gastaut syndrome, a severe childhood epilepsy with multiple seizure types that can be controlled with medication, currently experiencing a prolonged seizure state.
Coding Tips
- •Lennox-Gastaut is a specific, well-defined epilepsy syndrome; ensure diagnosis is confirmed before coding
- •Status epilepticus in this syndrome is particularly dangerous and requires emergency management
Clinical Significance
Lennox-Gastaut syndrome is a severe childhood-onset epilepsy characterized by multiple seizure types (tonic, atonic, atypical absence), slow spike-and-wave EEG pattern, and intellectual disability. Status epilepticus in LGS is particularly dangerous and may present as non-convulsive status. This syndrome carries significant lifelong morbidity and requires comprehensive multidisciplinary management.
Documentation Requirements
- ✓Confirmed diagnosis of Lennox-Gastaut syndrome by neurologist
- ✓Documentation of characteristic features: multiple seizure types, cognitive impairment, EEG findings
- ✓Active status epilepticus during the encounter
- ✓Statement that condition responds to medication (not intractable)
- ✓Current antiepileptic drug regimen
- ✓Emergency interventions for status epilepticus
Commonly Confused Codes
G40.812 — Lennox-Gastaut, not intractable, WITHOUT status epilepticusG40.813 — Lennox-Gastaut, INTRACTABLE, with status epilepticusG40.821 — Epileptic spasms with status epilepticus; LGS may evolve from infantile spasms but is a distinct diagnosisG40.401 — Other generalized epilepsy with status epilepticus; use when LGS criteria are NOT metG40.801 — Other epilepsy with status epilepticus; less specific than LGS
Code Hierarchy
└G40Epilepsy and recurrent seizures└G40.8Other epilepsy and recurrent seizures└G40.81Lennox-Gastaut syndrome└G40.811Lennox-Gastaut syndrome, not intractable, with status epilepticus
└G40.811Lennox-Gastaut syndrome, not intractable, with status epilepticus