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G37.5

Billable

Concentric sclerosis [Balo] of central nervous system

HCC Category Mapping

V28HCC 198Multiple Sclerosis
0.000
V24HCC 77Multiple Sclerosis
0.476
ESRDHCC 77Multiple Sclerosis
0.000
RxHCCHCC 159Multiple Sclerosis
0.000

What This Code Means

A rare neurological condition where inflammation and damage to nerve insulation (myelin) occurs in concentric rings in the brain and spinal cord, also known as Balo's disease.

Coding Tips

  • This is a rare demyelinating disease; ensure diagnosis is confirmed by neuroimaging and clinical presentation before coding
  • Do not confuse with other demyelinating diseases like multiple sclerosis; documentation should specify 'concentric sclerosis' or 'Balo disease'

Clinical Significance

Concentric sclerosis (Balo disease) is a rare demyelinating disease characterized by concentric rings of alternating demyelinated and myelinated tissue on brain imaging. Originally considered a variant of multiple sclerosis, it is now recognized as a distinct entity with characteristic imaging findings. Accurate identification is important for treatment planning and risk adjustment.

Documentation Requirements

  • Documentation specifically identifying concentric sclerosis or Balo disease
  • MRI showing characteristic concentric ring or onion-skin pattern of demyelination
  • Neurological examination documenting associated deficits
  • Clinical timeline documenting disease course
  • Evidence distinguishing from multiple sclerosis and other demyelinating conditions
  • Current treatment plan (corticosteroids, immunosuppressants)

Commonly Confused Codes

Code Hierarchy

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