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G37.2

Billable

Central pontine myelinolysis

HCC Category Mapping

V28HCC 198Multiple Sclerosis
0.000
V24HCC 77Multiple Sclerosis
0.476
ESRDHCC 77Multiple Sclerosis
0.000

What This Code Means

A rare condition where the pons (a critical part of the brainstem) is damaged due to osmotic imbalance, typically from rapid sodium correction, causing paralysis and neurological symptoms.

Coding Tips

  • Document the precipitating cause, usually rapid correction of hyponatremia or hypernatremia
  • Review laboratory values and fluid management history to support diagnosis

Clinical Significance

Central pontine myelinolysis (osmotic demyelination syndrome) is a serious neurological condition where the myelin sheath in the pons is destroyed, usually due to rapid correction of hyponatremia. It can cause devastating consequences including locked-in syndrome. Accurate coding captures both the severity of the condition and the iatrogenic nature, which has important quality-of-care implications.

Documentation Requirements

  • Documentation specifying central pontine myelinolysis or osmotic demyelination syndrome
  • MRI findings showing characteristic pontine demyelination lesion
  • Documentation of the precipitating cause (rapid sodium correction, hyponatremia management)
  • Serial sodium laboratory values demonstrating the rate of correction
  • Neurological examination documenting quadriparesis, dysarthria, dysphagia, or other brainstem findings
  • Treatment plan and rehabilitation goals

Commonly Confused Codes

Code Hierarchy

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