G11.4
BillableHereditary spastic paraplegia
HCC Category Mapping
V28HCC 200 — Cerebellar Ataxia and Other Degenerative Diseases of Nervous System
0.262V24HCC 72 — Spinal Cord Disorders/Injuries
0.464ESRDHCC 72 — Spinal Cord Disorders/Injuries
0.000What This Code Means
Hereditary spastic paraplegia is an inherited disorder causing progressive stiffness and weakness in the legs due to degeneration of nerve fibers in the spinal cord.
Coding Tips
- •Document the inheritance pattern (autosomal dominant, recessive, or X-linked) if known
- •Specify the SPG type if genetically confirmed for more precise documentation
Clinical Significance
Hereditary spastic paraplegia is a group of inherited disorders causing progressive lower extremity spasticity and weakness due to corticospinal tract degeneration. Over 80 genetic subtypes exist, and the condition significantly impacts mobility and quality of life, driving ongoing needs for physical therapy, assistive devices, and specialist neurology care.
Documentation Requirements
- ✓Family history consistent with hereditary transmission
- ✓Progressive spasticity and weakness primarily in lower extremities
- ✓Neurological examination documenting upper motor neuron signs (hyperreflexia, clonus, Babinski)
- ✓Inheritance pattern if known (autosomal dominant, recessive, or X-linked)
- ✓Genetic testing results with SPG subtype if available
- ✓Gait analysis and current mobility status
Commonly Confused Codes
G04.1 — Tropical spastic paraplegia: caused by HTLV-1 infection, not inheritedG82.20 — Paraplegia, unspecified: a symptom code, not appropriate when hereditary spastic paraplegia is diagnosedG35 — Multiple sclerosis: can cause spastic paraplegia but is an acquired demyelinating diseaseG11.11 — Friedreich ataxia: hereditary but primarily ataxic rather than spastic presentation