G11.19
BillableOther early-onset cerebellar ataxia
HCC Category Mapping
V28HCC 200 — Cerebellar Ataxia and Other Degenerative Diseases of Nervous System
0.262V24HCC 72 — Spinal Cord Disorders/Injuries
0.464ESRDHCC 72 — Spinal Cord Disorders/Injuries
0.000What This Code Means
Other early-onset cerebellar ataxia refers to various inherited or genetic disorders affecting balance and coordination that begin in childhood or early adulthood.
Coding Tips
- •Document the specific diagnosis if known (e.g., ataxia-telangiectasia, SCADD) rather than using this unspecified code
- •Use this code only when a more specific early-onset ataxia code does not apply
Clinical Significance
Other early-onset cerebellar ataxia captures specific inherited ataxia subtypes that begin in childhood or early adulthood but do not have their own unique ICD-10 code, such as ataxia-telangiectasia or spinocerebellar ataxia with early onset. These conditions require lifelong neurological care, genetic counseling, and management of associated systemic complications.
Documentation Requirements
- ✓Specific ataxia diagnosis name documented (ataxia-telangiectasia, early-onset spinocerebellar ataxia, etc.)
- ✓Age of onset confirming early-onset classification
- ✓Progressive cerebellar symptoms on neurological examination
- ✓Genetic testing or diagnostic confirmation if available
- ✓Documentation that the condition does not meet criteria for Friedreich ataxia (G11.11)
- ✓Associated systemic manifestations documented and coded separately
Commonly Confused Codes
G11.11 — Friedreich ataxia: the most common early-onset ataxia with specific code; must be excluded firstG11.10 — Early-onset cerebellar ataxia, unspecified: use only when the specific type is truly unknownG11.3 — Cerebellar ataxia with defective DNA repair: ataxia-telangiectasia has its own specific code hereG11.8 — Other hereditary ataxias: for hereditary ataxias that do not fit early-onset or late-onset categories
Code Hierarchy
└G11Hereditary ataxia└G11.1Early-onset cerebellar ataxia└G11.19Other early-onset cerebellar ataxia
└G11.19Other early-onset cerebellar ataxia