E84.8
BillableCystic fibrosis with other manifestations
HCC Category Mapping
V28HCC 277 — Cystic Fibrosis
0.405V24HCC 110 — Cystic Fibrosis
0.473ESRDHCC 110 — Cystic Fibrosis
0.000RxHCCHCC 225 — Cystic Fibrosis
0.000What This Code Means
This code is used for cystic fibrosis when it affects other body systems beyond the lungs and intestines, such as the liver, sweat glands, or reproductive system.
Coding Tips
- •Specify which organ system is affected in documentation to support medical necessity and justify treatment decisions
- •Do not use this code if pulmonary or intestinal manifestations are the primary focus; use more specific codes instead
Clinical Significance
Cystic fibrosis with other manifestations captures CF involvement beyond the pulmonary and intestinal systems, including CF-related diabetes, hepatobiliary disease, male infertility, nasal polyps, and musculoskeletal complications. These multi-system effects reflect the complex nature of CF management.
Documentation Requirements
- ✓Confirmed cystic fibrosis diagnosis
- ✓Specific non-pulmonary, non-intestinal manifestation documented (CF-related diabetes, liver disease, infertility, sinusitis, arthropathy)
- ✓Current management of the specific manifestation
- ✓Explanation of why the manifestation is attributed to CF rather than a separate condition
- ✓Overall CF disease status and complexity documentation
Commonly Confused Codes
E84.0 — Cystic fibrosis with pulmonary manifestations: for lung involvement specificallyE84.19 — Cystic fibrosis with other intestinal manifestations: for GI involvement specificallyE84.9 — Cystic fibrosis, unspecified: less specific; use E84.8 when a specific non-pulmonary/non-GI manifestation is documentedE13.9 — Other specified diabetes mellitus: CF-related diabetes may use both E84.8 and an E13 code
Code Hierarchy
└E84Cystic fibrosis└E84.8Cystic fibrosis with other manifestations
└E84.8Cystic fibrosis with other manifestations