E84.19
BillableCystic fibrosis with other intestinal manifestations
HCC Category Mapping
V28HCC 277 — Cystic Fibrosis
0.405V24HCC 110 — Cystic Fibrosis
0.473ESRDHCC 110 — Cystic Fibrosis
0.000RxHCCHCC 225 — Cystic Fibrosis
0.000What This Code Means
This code covers cystic fibrosis with various intestinal problems other than meconium ileus, such as pancreatic insufficiency, distal intestinal obstruction, or malabsorption.
Coding Tips
- •Use this code for CF-related GI manifestations that are not meconium ileus; document the specific intestinal complication in the medical record
- •Consider coding pancreatic insufficiency separately if it's a significant component of the clinical picture
Clinical Significance
This code captures cystic fibrosis with intestinal manifestations other than meconium ileus, including distal intestinal obstruction syndrome (DIOS), rectal prolapse, malabsorption, and steatorrhea. GI involvement affects nutritional status and requires pancreatic enzyme replacement therapy and nutritional monitoring.
Documentation Requirements
- ✓Confirmed cystic fibrosis diagnosis
- ✓Specific intestinal manifestation documented (DIOS, malabsorption, steatorrhea, rectal prolapse, constipation)
- ✓Pancreatic enzyme replacement therapy regimen
- ✓Nutritional status and BMI assessment
- ✓Fat-soluble vitamin levels and supplementation
- ✓Documentation that this is NOT meconium ileus (which has its own code E84.11)
Commonly Confused Codes
E84.11 — Meconium ileus in cystic fibrosis: specific intestinal manifestation with its own codeE84.0 — Cystic fibrosis with pulmonary manifestations: for lung involvement; code both if applicableE84.8 — Cystic fibrosis with other manifestations: for non-pulmonary, non-intestinal CF manifestationsK90.0 — Celiac disease: separate malabsorption condition unrelated to CF
Code Hierarchy
└E84Cystic fibrosis└E84.1Cystic fibrosis with intestinal manifestations└E84.19Cystic fibrosis with other intestinal manifestations
└E84.19Cystic fibrosis with other intestinal manifestations