E83.19
BillableOther disorders of iron metabolism
HCC Category Mapping
RxHCCHCC 43 — Other Significant Endocrine and Metabolic Disorders
0.000What This Code Means
Problems with how the body processes and uses iron that don't fit into other specific iron metabolism categories.
Coding Tips
- •Review documentation carefully to determine if a more specific iron metabolism code applies
- •This code is appropriate for rare or atypical iron metabolism disorders
Clinical Significance
This code captures iron metabolism disorders that are not classified as hemochromatosis, such as sideroblastic anemia-related iron loading or other rare iron transport deficiencies. It reflects metabolic dysfunction that may require ongoing management and monitoring.
Documentation Requirements
- ✓Specific iron metabolism disorder identified by the provider
- ✓Laboratory results supporting the diagnosis (iron studies, ferritin, TIBC)
- ✓Clinical manifestations and affected organ systems
- ✓Distinction from hemochromatosis and iron deficiency
- ✓Treatment plan addressing the iron metabolism disorder
Use Additional Code
- code, if applicable, for idiopathic pulmonary hemosiderosis (J84.03)
Commonly Confused Codes
E83.110 — Hereditary hemochromatosis: a specific iron overload condition with HCC mapping; do not use E83.19 for hemochromatosisE83.118 — Other hemochromatosis: use for non-hereditary hemochromatosis specificallyE61.1 — Iron deficiency: opposite direction of iron metabolism dysfunctionD50.9 — Iron deficiency anemia, unspecified: anemia from iron deficiency, distinct from iron metabolism disorders
Code Hierarchy
└E83Disorders of mineral metabolism└E83.1Disorders of iron metabolism└E83.19Other disorders of iron metabolism
└E83.19Other disorders of iron metabolism