E83.00
BillableDisorder of copper metabolism, unspecified
HCC Category Mapping
V28HCC 50 — Glycogen/Amino-Acid/Other Metabolic Disorders
0.289RxHCCHCC 42 — Endocrine Disorders and Metabolic Conditions
0.000What This Code Means
A metabolic disorder affecting copper levels in the body where the specific type or cause has not been identified.
Coding Tips
- •This is a non-specific code; attempt to identify the specific copper metabolism disorder before using this code
- •Review for Wilson's disease (E83.01) or other specified copper disorders that may be more appropriate
Clinical Significance
Disorder of copper metabolism, unspecified is used when abnormal copper metabolism is confirmed but the specific condition (Wilson disease, Menkes disease) has not been identified. Copper metabolism disorders can cause severe hepatic, neurological, and psychiatric disease, making prompt identification critical for treatment initiation.
Documentation Requirements
- ✓Provider documentation confirming a copper metabolism disorder
- ✓Copper studies: serum ceruloplasmin, serum copper, 24-hour urine copper
- ✓Reason for lack of specificity (evaluation in progress, indeterminate results)
- ✓Hepatic assessment: liver function tests, imaging
- ✓Neurological assessment if symptoms present
- ✓Plan for further diagnostic workup to determine specific copper disorder
Commonly Confused Codes
E83.01 — Wilson's disease: specific copper overload disorder with ceruloplasmin deficiencyE83.09 — Other disorders of copper metabolism: for identified copper disorders other than Wilson'sE61.0 — Copper deficiency: nutritional copper deficiency, not an inherited metabolism disorderE83.10 — Disorder of iron metabolism, unspecified: different metal metabolism, do not confuse
Code Hierarchy
└E83Disorders of mineral metabolism└E83.0Disorders of copper metabolism└E83.00Disorder of copper metabolism, unspecified
└E83.00Disorder of copper metabolism, unspecified