E78.70
BillableDisorder of bile acid and cholesterol metabolism, unspecified
HCC Category Mapping
RxHCCHCC 47 — Disorders of Fatty-Acid and Lipid Metabolism
0.000What This Code Means
A disorder affecting how the body processes bile acids and cholesterol, but the specific type is not identified.
Coding Tips
Clinical Significance
Disorder of bile acid and cholesterol metabolism, unspecified covers conditions where bile acid synthesis or cholesterol metabolic pathways are disrupted but the specific defect has not been identified. Bile acid synthesis disorders can cause cholestatic liver disease, fat malabsorption, and fat-soluble vitamin deficiency, often presenting in infancy or childhood.
Documentation Requirements
- ✓Provider documentation of confirmed bile acid or cholesterol metabolism disorder
- ✓Diagnostic testing: serum bile acid profile, urine bile acid analysis, or genetic testing
- ✓Clinical manifestations: cholestatic jaundice, hepatomegaly, steatorrhea, fat-soluble vitamin deficiency
- ✓Reason for lack of specificity (workup in progress, indeterminate results)
- ✓Treatment plan: bile acid replacement therapy (cholic acid), fat-soluble vitamin supplementation
Commonly Confused Codes
E78.79 — Other disorders of bile acid and cholesterol metabolism: use when a specific disorder is identifiedK83.1 — Obstruction of bile duct: mechanical obstruction, not a metabolic disorderE78.00 — Pure hypercholesterolemia: elevated circulating cholesterol, different from cholesterol metabolism pathway defectsE80.7 — Disorder of bilirubin metabolism, unspecified: bilirubin metabolism is separate from bile acid metabolism
Code Hierarchy
└E78Disorders of lipoprotein metabolism and other lipidemias└E78.7Disorders of bile acid and cholesterol metabolism└E78.70Disorder of bile acid and cholesterol metabolism, unspecified
└E78.70Disorder of bile acid and cholesterol metabolism, unspecified