E76.9
BillableGlucosaminoglycan metabolism disorder, unspecified
HCC Category Mapping
V24HCC 23 — Other Significant Endocrine and Metabolic Disorders
0.230ESRDHCC 23 — Other Significant Endocrine and Metabolic Disorders
0.000RxHCCHCC 43 — Other Significant Endocrine and Metabolic Disorders
0.000What This Code Means
Glucosaminoglycan metabolism disorder, unspecified, is used when a patient has a disorder affecting how the body processes complex sugars but the specific type cannot be identified.
Coding Tips
- •This is the least specific code in the glucosaminoglycan metabolism category; pursue additional diagnostic information when possible
- •Use only when no more specific diagnosis code can be determined from the clinical documentation
Clinical Significance
Glucosaminoglycan metabolism disorder, unspecified is used when abnormal GAG metabolism is confirmed but the specific disorder has not been identified. This is a broad code that may capture early diagnostic evaluations for suspected MPS or other GAG disorders before definitive testing is complete.
Documentation Requirements
- ✓Provider documentation of confirmed or suspected GAG metabolism disorder
- ✓Supporting clinical or laboratory evidence (elevated urine GAGs, clinical features suggestive of storage disorder)
- ✓Reason for lack of specificity (evaluation in progress, atypical results)
- ✓Plan for further diagnostic evaluation
- ✓Current symptom management
Commonly Confused Codes
E76.3 — Mucopolysaccharidosis, unspecified: more specific than E76.9 when MPS IS confirmed but type unknownE76.8 — Other disorders of glucosaminoglycan metabolism: for identified non-MPS GAG disordersE88.9 — Metabolic disorder, unspecified: even broader and should not be used when GAG involvement is knownE76.01-E76.29 — Specific MPS types: use whenever the type is identified
Code Hierarchy
└E76Disorders of glycosaminoglycan metabolism└E76.9Glucosaminoglycan metabolism disorder, unspecified
└E76.9Glucosaminoglycan metabolism disorder, unspecified