E76.211 ICD-10-CM Code: Morquio B mucopolysaccharidoses
E76.211 maps to CMS-HCC V28 49 (RAF 9.256). Documentation must support MEAT. MEAT criteria · RAF calculator · HCC Buddy coding tools
HCC Buddy Code Card
Digital ICD-10 code-book layout with official code detail, always-visible risk models, Code Trumping, and Buddy coding guidance.
FY 2026 Apr update / Endocrine, nutritional and metabolic diseases (E00-E89) / Metabolic disorders (E70-E88)
E76.211
Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidanceMorquio B mucopolysaccharidoses
Morquio B mucopolysaccharidosis is a rare inherited metabolic disorder similar to Morquio A but caused by a different enzyme deficiency, resulting in skeletal abnormalities and progressive physical limitations.
Buddy Insight
Morquio B mucopolysaccharidosis (MPS IVB) is caused by beta-galactosidase deficiency, leading to keratan sulfate accumulation with a clinical phenotype similar to Morquio A but generally milder.
CMS-HCC V28
MappedHCC 49
RAF 9.256
CMS-HCC V24
MappedHCC 23
RAF 0.194
ACA/HHS
MappedHCC 26
Varies by metal level
ESRD/PACE
MappedHCC 23
RAF 0.036
RXHCC
MappedHCC 41
RAF 3.081
Code Book Path
Inclusion Terms
Official- Morquio-like mucopolysaccharidoses
- Morquio-like syndrome
- Morquio syndrome B
- Mucopolysaccharidosis, type IVB
Excludes 2
OfficialICD-10-CM does not list Excludes 2 notes for E76.211 in this effective period.
Related Child Codes
Includes
OfficialICD-10-CM does not list Includes notes for E76.211 in this effective period.
Excludes 1
OfficialICD-10-CM does not list Excludes 1 notes for E76.211 in this effective period.
Code First
OfficialICD-10-CM does not list Code First sequencing instructions for E76.211 in this effective period.
Use Additional
OfficialICD-10-CM does not list Use Additional Code instructions for E76.211 in this effective period.
Code Also
OfficialICD-10-CM does not list Code Also instructions for E76.211 in this effective period.
Buddy Documentation Tip
MEAT Support
Audit Caution
Common Mistakes
Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →
Is E76.211 an HCC code?
Yes. E76.211 (Morquio B mucopolysaccharidoses) maps to Specified Lysosomal Storage Disorders under the CMS-HCC V28 risk adjustment model (and Other Significant Endocrine and Metabolic Disorders under V24), with a community non-dual aged RAF of 9.256. It is billable for payment year 2026.
Coder answer: E76.211 is billable and maps to V28 HCC 49, Specified Lysosomal Storage Disorders. Open it in the Code Book for the tabular path, RAF, and MEAT checklist.
- Code
- E76.211
- Description
- Morquio B mucopolysaccharidoses
- HCC (V28)
- HCC 49 — Specified Lysosomal Storage Disorders
- RAF
- 9.256
- Billable
- Yes
- Payment year
- 2026
HCC Category Mapping
Each model's RAF is its CMS base weight for that model's standard population, so weights are not directly comparable across models: CMS-HCC V28 and V24 use Community, Non-Dual, Aged; ESRD uses the dialysis continuing-enrollee model; RxHCC is the Part D continuing-enrollee, non-low-income, aged weight (a larger scale than CMS-HCC). ACA/HHS has no single weight — it varies by metal level. Actual per-patient RAF contribution depends on member segment, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains in use during the transition and for historical data.
Work E76.211 in the Code Book — tabular path, V28 RAF, and MEAT checklist →
MEAT Criteria for E76.211
For E76.211 to count as a valid HCC diagnosis in a given encounter, the provider's documentation must show MEAT: Monitor, Evaluate, Assess, or Treat. A diagnosis from a prior year does not carry forward automatically, it has to be re-documented and supported each calendar year.
- MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
- EEvaluate: test results, medication response, or physical findings reviewed by the provider
- AAssess: explicit mention in the assessment or plan with acknowledgment of status
- TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis
Only one of M/E/A/T is required to support the code, but the documentation must be specific enough to show that the provider actually addressed E76.211 during that encounter, not just copy-forwarded from a problem list.
Coder workflow notes
Get the V28 RAF + MEAT cheat sheet
One printable page: confirm a code's V28 HCC status, its RAF weight, and the MEAT your note needs to make it stick. Free, no card.
Free PDF. No card. Unsubscribe anytime.
What This Code Means
E76.211 is the ICD-10-CM diagnosis code for morquio b mucopolysaccharidoses. Morquio B mucopolysaccharidosis is a rare inherited metabolic disorder similar to Morquio A but caused by a different enzyme deficiency, resulting in skeletal abnormalities and progressive physical limitations. E76.211 sits in the ICD-10-CM chapter for endocrine, nutritional and metabolic diseases (e00-e89), within the section covering metabolic disorders (e70-e88).
Under the CMS-HCC V28 risk adjustment model, E76.211 maps to Specified Lysosomal Storage Disorders (HCC 49) with a community, non-dual, aged base RAF weight of 9.256. Under the older CMS-HCC V24 model, E76.211 maps to Other Significant Endocrine and Metabolic Disorders (HCC 23) with a community, non-dual, aged base RAF weight of 0.194. V28 is the CMS-HCC risk adjustment model that reached 100% phase-in for payment year 2026, replacing V24 which was used during the PY2024–PY2025 transition.
Morquio B is less common than Morquio A; verify the specific enzyme deficiency is documented to ensure correct code selection. Because E76.211 maps to a payment HCC, the provider's documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's Medicare Advantage risk adjustment score. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.
HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for E76.211 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.
Coding Tips
- •Morquio B is less common than Morquio A; verify the specific enzyme deficiency is documented to ensure correct code selection
- •Document the degree of skeletal involvement and any systemic complications for complete clinical picture
Clinical Significance
Morquio B mucopolysaccharidosis (MPS IVB) is caused by beta-galactosidase deficiency, leading to keratan sulfate accumulation with a clinical phenotype similar to Morquio A but generally milder. Distinguishing Morquio B is important because it shares an enzyme deficiency with GM1 gangliosidosis, and treatment approaches may differ from Morquio A.
Documentation Requirements
- ✓Specific diagnosis of Morquio B syndrome (MPS IVB) documented
- ✓Confirmatory enzyme assay showing beta-galactosidase deficiency or GLB1 gene mutation analysis
- ✓Documentation distinguishing this from GM1 gangliosidosis (which shares the same enzyme deficiency but has different clinical features)
- ✓Skeletal manifestations and severity assessment
- ✓Current treatment and management plan
Commonly Confused Codes
- •E76.210: Morquio A (MPS IVA): different enzyme (GALNS) but similar skeletal phenotype
- •E76.219: Morquio, unspecified: avoid when B subtype is confirmed
- •E75.19: Other gangliosidoses (including GM1): shares beta-galactosidase deficiency but presents with neurodegeneration
- •E76.29: Other mucopolysaccharidoses: incorrect for Morquio B which has its own specific code