E74.89

HCC Category Mapping

What This Code Means

A metabolic disorder affecting how the body breaks down or processes carbohydrates (sugars and starches) that doesn't fit into other specific carbohydrate metabolism categories.

Coding Tips

• •Document the specific carbohydrate metabolism defect in the medical record for clarity
• •Review the medical record to ensure a more specific E74 code is not applicable before using this code

Clinical Significance

Other specified disorders of carbohydrate metabolism is a residual code capturing carbohydrate metabolism disorders that do not fit into specific categories for glycogen storage diseases, galactose disorders, or glucose transport defects. This includes conditions like essential fructosuria, hereditary fructose intolerance, and fructose-1,6-diphosphatase deficiency. Some of these can cause severe hypoglycemia and liver damage.

Documentation Requirements

• ✓Specific carbohydrate metabolism disorder identified by the provider
• ✓Laboratory confirmation including relevant enzyme assays or metabolic testing
• ✓Genetic testing results if available
• ✓Documentation of clinical manifestations and dietary triggers
• ✓Current dietary management plan including avoidance of specific carbohydrates

Commonly Confused Codes