E71.311 ICD-10-CM Code: Medium chain acyl CoA dehydrogenase deficiency
E71.311 is not a CMS-HCC payment code. MEAT criteria · RAF Calculator · free HCC coding tools
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FY 2026 Apr update / Endocrine, nutritional and metabolic diseases (E00-E89) / Metabolic disorders (E70-E88)
E71.311
Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidanceMedium chain acyl CoA dehydrogenase deficiency
A rare inherited metabolic disorder where the body lacks an enzyme needed to break down medium-chain fatty acids, potentially causing low blood sugar, liver problems, and muscle weakness.
Buddy Insight
Medium chain acyl-CoA dehydrogenase deficiency (MCAD) is the most common inherited fatty acid oxidation disorder, detected through newborn screening in most states.
CMS-HCC V28
N/A—
Not mapped
CMS-HCC V24
HistoricalHistorical
Not used for CY2026 payment
ACA/HHS
Context neededHCC 028
Coefficient needs member context
ESRD/PACE
Context neededHCC 23
Coefficient needs member context
RXHCC
MappedHCC 43
Code-level coefficient reference
Code Book Path
Inclusion Terms
Official- MCAD deficiency
Excludes 2
Official- Ehlers-Danlos syndromes (Q79.6-)Inherited from E70-E88, E71.3
- carnitine deficiency due to inborn error of metabolism (E71.42)Inherited from E70-E88, E71.3
Related Codes
Includes
OfficialNo Includes notes are included in this display for E71.311. Check the code and parent instructions in the Code Book.
Excludes 1
Official- transitory endocrine and metabolic disorders specific to newborn (P70-P74)Inherited from E00-E89, E70-E88, E71.3
- androgen insensitivity syndrome (E34.5-)Inherited from E00-E89, E70-E88, E71.3
- congenital adrenal hyperplasia (E25.0)Inherited from E00-E89, E70-E88, E71.3
- hemolytic anemias attributable to enzyme disorders (D55.-)Inherited from E00-E89, E70-E88, E71.3
- Marfan syndrome (Q87.4-)Inherited from E00-E89, E70-E88, E71.3
- 5-alpha-reductase deficiency (E29.1)Inherited from E00-E89, E70-E88, E71.3
- peroxisomal disorders (E71.5)Inherited from E00-E89, E70-E88, E71.3
- Refsum's disease (G60.1)Inherited from E00-E89, E70-E88, E71.3
- Schilder's disease (G37.0)Inherited from E00-E89, E70-E88, E71.3
Code First
OfficialNo Code First sequencing instructions are included in this display for E71.311. Check the code and parent instructions in the Code Book.
Use Additional
OfficialNo Use Additional Code instructions are included in this display for E71.311. Check the code and parent instructions in the Code Book.
Code Also
OfficialNo Code Also instructions are included in this display for E71.311. Check the code and parent instructions in the Code Book.
Buddy Documentation Tip
MEAT Support
Audit Caution
Common Mistakes
Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →
Is E71.311 an HCC code?
E71.311 has no mapping under the current CMS-HCC V28 community payment model. E71.311 has a separate mapping under the CMS-HCC ESRD model (HCC 23 (Other Significant Endocrine and Metabolic Disorders)) and the Part D RxHCC model (HCC 43 (Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders)); the applicable result needs member context. E71.311 also appears in the HHS-HCC commercial risk model (HCC 028 (HHS-HCC 028 child, RAF varies by metal level)), where the result depends on member context and is not a Medicare Advantage payment mapping.
- Code
- E71.311
- Description
- Medium chain acyl CoA dehydrogenase deficiency
- HCC (V28)
- No CMS-HCC V28 mapping
- RAF reference coefficient
- —
- Billable
- Yes
- Payment year
- 2026
HCC Category Mapping
These are source-labeled model coefficients, not member totals. A category may still be removed by hierarchy or model cleanup rules. Weights are not directly comparable across models: CMS-HCC V28 and V24 use Community, Non-Dual, Aged; ESRD uses the dialysis continuing-enrollee model; RxHCC is the Part D continuing-enrollee, non-low-income, aged weight (a larger scale than CMS-HCC). ACA/HHS has no single weight — it varies by metal level. Actual per-patient RAF contribution depends on member context, hierarchy and cleanup rules, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains available for historical review.
Work E71.311 in the Code Book — tabular path, V28 RAF reference, and MEAT checklist →
MEAT review for E71.311
For E71.311, confirm that the documentation supports the diagnosis and meets the applicable coding, encounter, program and payer requirements. MEAT (Monitor, Evaluate, Assess, or Treat) is a review mnemonic, not a universal CMS coding rule.
- MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
- EEvaluate: test results, medication response, or physical findings reviewed by the provider
- AAssess: explicit mention in the assessment or plan with acknowledgment of status
- TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis
Coder workflow notes
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What This Code Means
E71.311 is the ICD-10-CM diagnosis code for medium chain acyl coa dehydrogenase deficiency. A rare inherited metabolic disorder where the body lacks an enzyme needed to break down medium-chain fatty acids, potentially causing low blood sugar, liver problems, and muscle weakness. E71.311 sits in the ICD-10-CM chapter for endocrine, nutritional and metabolic diseases (e00-e89), within the section covering metabolic disorders (e70-e88).
E71.311 has no mapping under the current CMS-HCC V28 community payment model. E71.311 has a separate mapping under the CMS-HCC ESRD model (HCC 23 (Other Significant Endocrine and Metabolic Disorders)) and the Part D RxHCC model (HCC 43 (Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders)); the applicable result needs member context. E71.311 also appears in the HHS-HCC commercial risk model (HCC 028 (HHS-HCC 028 child, RAF varies by metal level)), where the result depends on member context and is not a Medicare Advantage payment mapping. Do not assign V28 risk adjustment value from this page; verify the applicable model and payment year before using this code for risk adjustment.
MCAD deficiency is one of the most common fatty acid oxidation disorders; ensure accurate documentation.
HCC Buddy maintains structured V28 and V24 mapping, source-labeled coefficient references, and MEAT documentation criteria for E71.311 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.
Coding Tips
- •MCAD deficiency is one of the most common fatty acid oxidation disorders; ensure accurate documentation
- •Note any acute episodes or complications such as hypoglycemia or encephalopathy for complete coding
Clinical Significance
Medium chain acyl-CoA dehydrogenase deficiency (MCAD) is the most common inherited fatty acid oxidation disorder, detected through newborn screening in most states. Patients cannot oxidize medium-chain fatty acids during fasting, creating risk of hypoketotic hypoglycemia, hepatic dysfunction, and potentially fatal metabolic crises. With proper management including avoidance of prolonged fasting, prognosis is excellent.
Documentation Requirements
- ✓Document newborn screening results or confirmatory testing (acylcarnitine profile showing elevated C8), genetic mutation analysis (common A985G mutation), history of metabolic decompensation episodes, and current fasting avoidance protocol.
- ✓Record any emergency management plans.