E71.310 ICD-10-CM Code: Long chain/very long chain acyl CoA dehydrogenase deficiency
HCC Buddy Code Card
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FY 2026 Apr update / Endocrine, nutritional and metabolic diseases (E00-E89) / Metabolic disorders (E70-E88)
E71.310
Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidanceLong chain/very long chain acyl CoA dehydrogenase deficiency
This is a rare inherited metabolic disorder where the body cannot properly break down certain fatty acids, leading to a buildup of toxic substances in the blood and tissues. This condition can cause muscle weakness, liver problems, and heart issues, especially during illness or fasting.
Buddy Insight
Long chain and very long chain acyl-CoA dehydrogenase deficiency (LCAD/VLCAD) impairs the body's ability to oxidize long-chain fatty acids for energy, particularly during fasting or physiological stress.
CMS-HCC V28
N/A—
Not mapped
CMS-HCC V24
MappedHCC 23
RAF 0.194
ACA/HHS
MappedHCC 28
Varies by metal level
ESRD/PACE
MappedHCC 23
RAF 0.036
RXHCC
MappedHCC 43
RAF 0.063
Code Book Path
Inclusion Terms
Official- LCAD deficiency
- VLCAD deficiency
Excludes 2
OfficialICD-10-CM does not list Excludes 2 notes for E71.310 in this effective period.
Related Child Codes
Includes
OfficialICD-10-CM does not list Includes notes for E71.310 in this effective period.
Excludes 1
OfficialICD-10-CM does not list Excludes 1 notes for E71.310 in this effective period.
Code First
OfficialICD-10-CM does not list Code First sequencing instructions for E71.310 in this effective period.
Use Additional
OfficialICD-10-CM does not list Use Additional Code instructions for E71.310 in this effective period.
Code Also
OfficialICD-10-CM does not list Code Also instructions for E71.310 in this effective period.
Buddy Documentation Tip
MEAT Support
Audit Caution
Common Mistakes
Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →
Is E71.310 an HCC code?
Yes. E71.310 maps to Other Significant Endocrine and Metabolic Disorders under the V24 model but is not retained in V28.
- Code
- E71.310
- Description
- Long chain/very long chain acyl CoA dehydrogenase deficiency
- HCC (V28)
- No CMS-HCC V28 mapping
- RAF
- —
- Billable
- Yes
- Payment year
- 2026
HCC Category Mapping
Each model's RAF is its CMS base weight for that model's standard population, so weights are not directly comparable across models: CMS-HCC V28 and V24 use Community, Non-Dual, Aged; ESRD uses the dialysis continuing-enrollee model; RxHCC is the Part D continuing-enrollee, non-low-income, aged weight (a larger scale than CMS-HCC). ACA/HHS has no single weight — it varies by metal level. Actual per-patient RAF contribution depends on member segment, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains in use during the transition and for historical data.
Work E71.310 in the Code Book — tabular path, V28 RAF, and MEAT checklist →
MEAT Criteria for E71.310
For E71.310 to count as a valid HCC diagnosis in a given encounter, the provider's documentation must show MEAT: Monitor, Evaluate, Assess, or Treat. A diagnosis from a prior year does not carry forward automatically, it has to be re-documented and supported each calendar year.
- MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
- EEvaluate: test results, medication response, or physical findings reviewed by the provider
- AAssess: explicit mention in the assessment or plan with acknowledgment of status
- TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis
Only one of M/E/A/T is required to support the code, but the documentation must be specific enough to show that the provider actually addressed E71.310 during that encounter, not just copy-forwarded from a problem list.
Coder workflow notes
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What This Code Means
E71.310 is the ICD-10-CM diagnosis code for long chain/very long chain acyl coa dehydrogenase deficiency. This is a rare inherited metabolic disorder where the body cannot properly break down certain fatty acids, leading to a buildup of toxic substances in the blood and tissues. This condition can cause muscle weakness, liver problems, and heart issues, especially during illness or fasting. E71.310 sits in the ICD-10-CM chapter for endocrine, nutritional and metabolic diseases (e00-e89), within the section covering metabolic disorders (e70-e88).
Under the older CMS-HCC V24 model, E71.310 maps to Other Significant Endocrine and Metabolic Disorders (HCC 23) with a community, non-dual, aged base RAF weight of 0.194. V28 is the CMS-HCC risk adjustment model that reached 100% phase-in for payment year 2026, replacing V24 which was used during the PY2024–PY2025 transition.
This is a specific subtype of fatty acid oxidation disorder - ensure you are not using the parent code E71.31 unless the specific type is truly unspecified. Because E71.310 maps to a payment HCC, the provider's documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's Medicare Advantage risk adjustment score. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.
HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for E71.310 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.
Coding Tips
- •This is a specific subtype of fatty acid oxidation disorder - ensure you are not using the parent code E71.31 unless the specific type is truly unspecified
- •Document any associated complications (cardiomyopathy, hepatomegaly, rhabdomyolysis) with additional codes, as this metabolic disorder often presents with multi-system involvement
Clinical Significance
Long chain and very long chain acyl-CoA dehydrogenase deficiency (LCAD/VLCAD) impairs the body's ability to oxidize long-chain fatty acids for energy, particularly during fasting or physiological stress. This condition carries significant risk of hypoketotic hypoglycemia, rhabdomyolysis, cardiomyopathy, and sudden death, especially in infancy. Newborn screening has improved early detection, but lifelong dietary management with medium-chain triglyceride supplementation is required.
Documentation Requirements
- ✓Document the specific chain-length deficiency (LCAD vs.
- ✓VLCAD), newborn screening results or confirmatory enzyme/genetic testing, acylcarnitine profiles, cardiac function assessments, and dietary management plan.
- ✓Record any episodes of rhabdomyolysis, hypoglycemia, or cardiac complications.
Commonly Confused Codes
- •E71.311 (Medium chain acyl CoA dehydrogenase deficiency
- •MCAD) which involves medium-chain rather than long-chain fatty acids; E71.312 (Short chain acyl CoA dehydrogenase deficiency
- •SCAD) involving short-chain fatty acids; E71.318 (Other disorders of fatty-acid oxidation) for unspecified oxidation defects.