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E70.311 ICD-10-CM Code: Autosomal recessive ocular albinism

E70.311 is not a CMS-HCC payment code. MEAT criteria · RAF Calculator · HCC coding software

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Code lookupE70.311

FY 2026 Apr update / Endocrine, nutritional and metabolic diseases (E00-E89) / Metabolic disorders (E70-E88)

E70.311

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Autosomal recessive ocular albinism

A rare inherited condition affecting only the eyes where melanin production is reduced, causing vision problems and light sensitivity, inherited when both parents carry the gene.

Buddy the Bee presenting code insight

Buddy Insight

Autosomal recessive ocular albinism is a rare inherited condition where reduced melanin production is confined to the eyes, affecting both males and females equally when both parents carry the gene mutation.

CMS-HCC V28

N/A

Not mapped

CMS-HCC V24

Historical

Historical

Not used for CY2026 payment

ACA/HHS

Context needed

HCC 028

Coefficient needs member context

ESRD/PACE

Context needed

HCC 23

Coefficient needs member context

RXHCC

HCC 43

Code-level coefficient reference

Inclusion Terms

Official

No inclusion terms are included in this display for E70.311. Check the code and parent instructions in the Code Book.

Excludes 2

Official
  • Ehlers-Danlos syndromes (Q79.6-)Inherited from E70-E88

Includes

Official

No Includes notes are included in this display for E70.311. Check the code and parent instructions in the Code Book.

Excludes 1

Official
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)Inherited from E00-E89, E70-E88
  • androgen insensitivity syndrome (E34.5-)Inherited from E00-E89, E70-E88
  • congenital adrenal hyperplasia (E25.0)Inherited from E00-E89, E70-E88
  • hemolytic anemias attributable to enzyme disorders (D55.-)Inherited from E00-E89, E70-E88
  • Marfan syndrome (Q87.4-)Inherited from E00-E89, E70-E88
  • 5-alpha-reductase deficiency (E29.1)Inherited from E00-E89, E70-E88

Code First

Official

No Code First sequencing instructions are included in this display for E70.311. Check the code and parent instructions in the Code Book.

Use Additional

Official

No Use Additional Code instructions are included in this display for E70.311. Check the code and parent instructions in the Code Book.

Code Also

Official

No Code Also instructions are included in this display for E70.311. Check the code and parent instructions in the Code Book.

Buddy Documentation Tip

HCC Buddy guidance
Documentation should include genetic testing results confirming autosomal recessive inheritance, detailed ophthalmologic examination (visual acuity, iris transillumination, fundoscopy, optical coherence tomography for foveal hypoplasia), and family history.
Normal or near-normal skin and hair pigmentation should be noted to distinguish from oculocutaneous forms.
Document all visual impairment management including corrective lenses and low-vision aids.

MEAT Support

HCC Buddy guidance
Documentation should include genetic testing results confirming autosomal recessive inheritance, detailed ophthalmologic examination (visual acuity, iris transillumination, fundoscopy, optical coherence tomography for foveal hypoplasia), and family history.
Normal or near-normal skin and hair pigmentation should be noted to distinguish from oculocutaneous forms.
Document all visual impairment management including corrective lenses and low-vision aids.

Audit Caution

HCC Buddy guidance
Confirm the autosomal recessive inheritance pattern through genetic testing or family history before using this specific code.
Do not confuse with X-linked ocular albinism, which predominantly affects males.
Code all vision complications separately.
Ensure documentation demonstrates that both parents are carriers if genetic testing has been performed on family members.

Common Mistakes

HCC Buddy guidance
E70.310 (X-linked ocular albinism) has a different inheritance pattern primarily affecting males.
E70.318 (Other ocular albinism) covers atypical variants.
E70.319 (Ocular albinism, unspecified) should not be used when the autosomal recessive pattern is confirmed.
E70.320-E70.329 (Oculocutaneous albinism) involves both skin and eyes.

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Is E70.311 an HCC code?

E70.311 is not in the CMS-HCC V28 or V24 community payment model. E70.311 has a separate mapping under the CMS-HCC ESRD model (HCC 23 (Other Significant Endocrine and Metabolic Disorders)) and the Part D RxHCC model (HCC 43 (Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders)); the applicable result needs member context. E70.311 also appears in the HHS-HCC commercial risk model (HCC 028 (HHS-HCC 028 child, RAF varies by metal level)), where the result depends on member context and is not a Medicare Advantage payment mapping.

Code
E70.311
Description
Autosomal recessive ocular albinism
HCC (V28)
No CMS-HCC V28 mapping
RAF reference coefficient
Billable
Yes
Payment year
2026

HCC Category Mapping

RxHCCHCC 43, Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders
Not separately weighted

These are source-labeled model coefficients, not member totals. A category may still be removed by hierarchy or model cleanup rules. Weights are not directly comparable across models: CMS-HCC V28 and V24 use Community, Non-Dual, Aged; ESRD uses the dialysis continuing-enrollee model; RxHCC is the Part D continuing-enrollee, non-low-income, aged weight (a larger scale than CMS-HCC). ACA/HHS has no single weight — it varies by metal level. Actual per-patient RAF contribution depends on member context, hierarchy and cleanup rules, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains available for historical review.

Work E70.311 in the Code Book — tabular path, V28 RAF reference, and MEAT checklist →

MEAT review for E70.311

For E70.311, confirm that the documentation supports the diagnosis and meets the applicable coding, encounter, program and payer requirements. MEAT (Monitor, Evaluate, Assess, or Treat) is a review mnemonic, not a universal CMS coding rule.

  • MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
  • EEvaluate: test results, medication response, or physical findings reviewed by the provider
  • AAssess: explicit mention in the assessment or plan with acknowledgment of status
  • TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Coder workflow notes

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What This Code Means

E70.311 is the ICD-10-CM diagnosis code for autosomal recessive ocular albinism. A rare inherited condition affecting only the eyes where melanin production is reduced, causing vision problems and light sensitivity, inherited when both parents carry the gene. E70.311 sits in the ICD-10-CM chapter for endocrine, nutritional and metabolic diseases (e00-e89), within the section covering metabolic disorders (e70-e88).

E70.311 has no mapping under the CMS-HCC V28 or V24 community payment models. E70.311 has a separate mapping under the CMS-HCC ESRD model (HCC 23 (Other Significant Endocrine and Metabolic Disorders)) and the Part D RxHCC model (HCC 43 (Pituitary, Adrenal Gland, and Other Endocrine and Metabolic Disorders)); the applicable result needs member context. E70.311 also appears in the HHS-HCC commercial risk model (HCC 028 (HHS-HCC 028 child, RAF varies by metal level)), where the result depends on member context and is not a Medicare Advantage payment mapping. Do not assign V28 risk adjustment value from this page; verify the applicable model and payment year before using this code for risk adjustment.

This autosomal recessive form can affect both males and females equally.

HCC Buddy maintains structured V28 and V24 mapping, source-labeled coefficient references, and MEAT documentation criteria for E70.311 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • This autosomal recessive form can affect both males and females equally
  • Document associated ocular manifestations such as reduced pigmentation of the iris or optic nerve hypoplasia

Clinical Significance

Autosomal recessive ocular albinism is a rare inherited condition where reduced melanin production is confined to the eyes, affecting both males and females equally when both parents carry the gene mutation. Patients experience decreased visual acuity, nystagmus, iris transillumination, and photophobia, though to a generally lesser degree than oculocutaneous albinism. Skin and hair pigmentation remain relatively normal.

Documentation Requirements

  • Documentation should include genetic testing results confirming autosomal recessive inheritance, detailed ophthalmologic examination (visual acuity, iris transillumination, fundoscopy, optical coherence tomography for foveal hypoplasia), and family history.
  • Normal or near-normal skin and hair pigmentation should be noted to distinguish from oculocutaneous forms.
  • Document all visual impairment management including corrective lenses and low-vision aids.

Commonly Confused Codes

  • E70.310 (X-linked ocular albinism) has a different inheritance pattern primarily affecting males.
  • E70.318 (Other ocular albinism) covers atypical variants.
  • E70.319 (Ocular albinism, unspecified) should not be used when the autosomal recessive pattern is confirmed.
  • E70.320-E70.329 (Oculocutaneous albinism) involves both skin and eyes.

Child Codes

Code Hierarchy

Also searched as

  • E70 311
  • E70311

Work E70.311 in HCC Buddy

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