E20.812
BillableAutoimmune hypoparathyroidism
HCC Category Mapping
V24HCC 23 — Other Significant Endocrine and Metabolic Disorders
0.230ESRDHCC 23 — Other Significant Endocrine and Metabolic Disorders
0.000RxHCCHCC 43 — Other Significant Endocrine and Metabolic Disorders
0.000What This Code Means
A condition where the immune system attacks and damages the parathyroid glands, preventing them from producing adequate parathyroid hormone.
Coding Tips
- •Document evidence of autoimmune involvement such as antibodies or associated autoimmune conditions
- •This code indicates an immune-mediated mechanism, distinguishing it from idiopathic hypoparathyroidism
Clinical Significance
E20.812 identifies autoimmune hypoparathyroidism, where the immune system attacks and destroys the parathyroid glands. This condition may occur in isolation or as part of autoimmune polyendocrine syndrome type 1 (APS-1/APECED syndrome), which also includes chronic mucocutaneous candidiasis and adrenal insufficiency. Early recognition is important for screening for associated autoimmune conditions.
Documentation Requirements
- ✓Documentation must include the diagnosis of autoimmune hypoparathyroidism with supporting evidence such as anti-parathyroid antibodies, low parathyroid hormone levels, hypocalcemia, and clinical context suggesting autoimmune etiology.
- ✓Evaluation for associated autoimmune conditions and any component of autoimmune polyendocrine syndrome should be documented.