Skip to content

D75.0 ICD-10-CM Code: Familial erythrocytosis

ICD-10-CM Code View

HCC Buddy Code Card

Digital ICD-10 code-book layout with official code detail, always-visible risk models, Code Trumping, and Buddy coding guidance.

FY 2026 Apr update / Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) / Other disorders of blood and blood-forming organs (D70-D77)

D75.0

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Familial erythrocytosis

An inherited genetic condition where the body produces too many red blood cells, present from birth or early life.

CMS-HCC V28

0

0

RAF 0

CMS-HCC V24

0

0

RAF 0

ACA/HHS

0

0

RAF 0

ESRD/PACE

0

0

RAF 0

RXHCC

0

0

RAF 0

Code Trumping

Basket needed

Code Book Path

Official
D75Other and unspecified diseases of blood and blood-forming organs
D75.0Familial erythrocytosis

Inclusion Terms

Official
  • Benign polycythemia
  • Familial polycythemia

Excludes 2

Official
  • acute lymphadenitis (L04.-)
  • chronic lymphadenitis (I88.1)
  • enlarged lymph nodes (R59.-)
  • hypergammaglobulinemia NOS (D89.2)
  • lymphadenitis NOS (I88.9)

Related Child Codes

Official
D75.1Secondary polycythemia
D75.8Other specified diseases of blood and blood-forming organs
D75.9Disease of blood and blood-forming organs, unspecified
D75.AGlucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia

Includes

Official

ICD-10-CM does not list Includes notes for D75.0 in this effective period.

Excludes 1

Official
  • hereditary ovalocytosis (D58.1)

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for D75.0 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for D75.0 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for D75.0 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance
This is a hereditary condition; document family history if available to support the diagnosis
Distinguish from secondary polycythemia (D75.1) which is acquired rather than inherited

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Is D75.0 an HCC code?

No. D75.0 is a billable ICD-10-CM code but does not map to any HCC category in V28, V24, ESRD, or RxHCC.

This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).

What This Code Means

D75.0 is the ICD-10-CM diagnosis code for familial erythrocytosis. An inherited genetic condition where the body produces too many red blood cells, present from birth or early life. D75.0 sits in the ICD-10-CM chapter for diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (d50-d89), within the section covering other disorders of blood and blood-forming organs (d70-d77).

D75.0 is a billable ICD-10-CM code but does not map to a payment HCC under the CMS-HCC V28, V24, ESRD, or RxHCC risk adjustment models. It can be reported on Medicare Advantage encounter data submissions but it does not contribute to a beneficiary's RAF score and therefore does not affect risk-adjusted payments to the plan.

This is a hereditary condition; document family history if available to support the diagnosis.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for D75.0 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • This is a hereditary condition; document family history if available to support the diagnosis
  • Distinguish from secondary polycythemia (D75.1) which is acquired rather than inherited

Excludes 1, Do NOT code together

  • hereditary ovalocytosis (D58.1)

Child Codes

Code Hierarchy

Work D75.0 in HCC Buddy

Open D75.0 in the Code Book for the full Index-to-Tabular path, MEAT checklist, and V28 HCC mapping, or in the Encoder to code from a keyword search. Pro includes 14 days to try everything.