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D74.0

Billable

Congenital methemoglobinemia

This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).

What This Code Means

This is a rare inherited blood condition where a person is born with an abnormality in their hemoglobin (the protein that carries oxygen in red blood cells), causing it to form methemoglobin which cannot effectively transport oxygen. This results in a bluish discoloration of the skin and lips, and reduced oxygen delivery to body tissues.

Coding Tips

  • •This is a congenital condition, so it should be coded even if the patient is an adult; verify documentation confirms the condition is present from birth rather than acquired later
  • •Do not confuse with acquired methemoglobinemia (D74.8) which results from exposure to certain drugs or chemicals; congenital cases are specifically D74.0

Code Hierarchy

└D74Methemoglobinemia└D74.0Congenital methemoglobinemia
└D74.0Congenital methemoglobinemia

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