D68.09

Billable

Other von Willebrand disease

HCC Category Mapping

V28HCC 112 — Von Willebrand Disease and Other Coagulation Defects

0.247

V24HCC 48 — Coagulation Defects and Other Specified Hematological Disorders

0.209

ESRDHCC 48 — Coagulation Defects and Other Specified Hematological Disorders

0.000

What This Code Means

A bleeding disorder related to von Willebrand factor that does not fit into the standard type 1, 2, or 3 classifications.

Coding Tips

•Use this code for atypical presentations or variants of von Willebrand disease not captured by more specific codes
•Document the specific characteristics or test results that led to this diagnosis to justify the use of the unspecified category

Clinical Significance

This code captures other specified forms of von Willebrand disease that do not fit into Types 1, 2, or 3 categories, including atypical presentations or mixed phenotypes. It may also be used for provisionally diagnosed VWD where complete subtyping has not yet been performed but certain features exclude the standard types.

Documentation Requirements

✓Document all VWF testing performed including antigen, activity, multimer analysis, and factor VIII levels.
✓Explain why the presentation does not fit standard types and what specific features distinguish this variant.
✓Record genetic testing results if available and the current treatment approach.

Code Also

, if applicable, qualitative platelet defects (D69.1)

Commonly Confused Codes

D68.00 (Von Willebrand disease, unspecified) — used when no subtyping has been attempted versus D68.09 which implies testing was done but doesn't fit standard categories D68.01-D68.03 (Specific types) — should be used when the phenotype clearly matches a standard type.

Code Hierarchy

└D68Other coagulation defects └D68.0Von Willebrand disease └D68.09Other von Willebrand disease

└D68.09Other von Willebrand disease