D68.029

Billable

Von Willebrand disease, type 2, unspecified

HCC Category Mapping

V28HCC 112 — Von Willebrand Disease and Other Coagulation Defects

0.247

V24HCC 48 — Coagulation Defects and Other Specified Hematological Disorders

0.209

ESRDHCC 48 — Coagulation Defects and Other Specified Hematological Disorders

0.000

What This Code Means

A bleeding disorder caused by abnormal von Willebrand factor protein (type 2), but the specific subtype is not specified or documented.

Coding Tips

•Use this code only when type 2 is confirmed but the specific variant (2A, 2B, 2M, 2N) cannot be determined from documentation
•Query the provider if additional testing results are available to specify the exact type 2 variant

Clinical Significance

Von Willebrand disease type 2, unspecified, captures cases where Type 2 VWD has been diagnosed through qualitative VWF defects but the specific subtype (2A, 2B, 2M, or 2N) has not been determined. Type 2 variants collectively account for approximately 20-25% of all VWD cases and generally present with more clinically significant bleeding than Type 1.

Documentation Requirements

✓Document VWF testing showing qualitative defect (disproportionate activity-to-antigen ratio), multimer analysis if available, and factor VIII levels.
✓Record current bleeding severity and treatment approach.
✓Query the provider to determine the specific subtype when additional testing has been performed.

Commonly Confused Codes

D68.020-D68.023 (Specific Type 2 subtypes) — should be used when the subtype is documented D68.00 (Von Willebrand disease, unspecified) — even more nonspecific and should be avoided when Type 2 is known D68.01 (Type 1) — quantitative deficiency without the qualitative defect seen in Type 2.

Code Hierarchy

└D68Other coagulation defects └D68.0Von Willebrand disease └D68.02Von Willebrand disease, type 2 └D68.029Von Willebrand disease, type 2, unspecified

└D68.029Von Willebrand disease, type 2, unspecified