What is ICD-10 code D68.023?

D68.023 is the ICD-10-CM diagnosis code for Von Willebrand disease, type 2N. It belongs to the ICD-10-CM chapter for diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (d50-d89). D68.023 is a billable code, meaning it can be reported on a claim as a primary or secondary diagnosis when supported by documentation. D68.023 is part of the FY2026 ICD-10-CM code set published by the CMS National Center for Health Statistics and used on Medicare, Medicaid, and commercial claims in the United States.

Yes. D68.023 is a billable ICD-10-CM code that can be reported on professional and institutional claims as a primary or secondary diagnosis when the provider documentation supports the specific condition described. Billable codes in ICD-10-CM are coded to the highest level of specificity available for the documented diagnosis. D68.023 is current for fiscal year 2026 and remains in the active CMS ICD-10-CM code set published by the National Center for Health Statistics.

Which HCC does D68.023 map to under V28?

D68.023 maps to CMS-HCC V28 HCC 112 (Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions). The category numbers, labels, and conditions come from the CMS-HCC V28 model file for payment year 2026.

What documentation supports D68.023?

Verify the specific type of von Willebrand disease (type 1, 2A, 2B, 2M, 2N, or 3) is documented in the medical record before assigning this code, as each type has a distinct ICD-10-CM code This code may be used alongside procedure codes for von Willebrand factor testing or treatment codes (such as desmopressin administration) depending on the clinical encounter Because D68.023 maps to an HCC category, the documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) before the diagnosis is used for risk adjustment. See the MEAT criteria checklist at /meat-criteria for what Monitor, Evaluate, Assess, or Treat looks like in a note. MEAT is generic documentation evidence, not a payer-specific rule.

2026 ICD-10-CM D68.023: Von Willebrand disease

D68.023 maps to CMS-HCC V28 112. A source-labeled RAF reference is available. Documentation must support MEAT. MEAT criteria · RAF Calculator · HCC coding software

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Code lookupD68.023Effective periodFY2026 Apr Update (Apr 1-Sep 30)

FY 2026 Apr update / Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) / Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)

D68.023

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Von Willebrand disease, type 2N

Von Willebrand disease type 2N is a bleeding disorder where the body produces abnormal von Willebrand factor protein that doesn't work properly, causing difficulty with blood clotting and increased bleeding tendency. This specific type involves a defect in how the von Willebrand factor binds to platelets.

Buddy Insight

Von Willebrand disease type 2N (Normandy variant) is characterized by markedly reduced VWF binding affinity for factor VIII, resulting in accelerated factor VIII clearance and low factor VIII levels.

CMS-HCC V28

Mapped

HCC 112

Immune Thrombocytopenia and S...

Code-level coefficient reference

CMS-HCC V24

Historical

Not used for standard CY2026 Medicare Advantage payment. Select a historical period to review V24.

Not used for CY2026 payment

ACA/HHS

Mapped

HCC 075

HHS-HCC 075 adult, RAF varies...

Code-level coefficient reference

ESRD/PACE

Mapped

HCC 48

Coagulation Defects and Other...

Code-level coefficient reference

RXHCC

N/A

—

Not risk-adjusted for this model/period.

Not mapped

Code Book Path

Official

D68.0Von Willebrand disease

D68.02Von Willebrand disease, type 2

D68.023Von Willebrand disease, type 2N

Inclusion Terms

Official

Qualitative defects of von Willebrand factor with defective von Willebrand factor to factor VIII binding
Qualitative defects of von Willebrand factor with markedly decreased affinity for factor VIII

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for D68.023 in this effective period.

Related Child Codes

Official

D68.020Von Willebrand disease, type 2A

D68.021Von Willebrand disease, type 2B

D68.022Von Willebrand disease, type 2M

D68.029Von Willebrand disease, type 2, unspecified

Includes

Official

ICD-10-CM does not list Includes notes for D68.023 in this effective period.

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for D68.023 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for D68.023 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for D68.023 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for D68.023 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance

Document VWF:factor VIII binding assay results showing reduced binding capacity, low factor VIII levels with relatively normal VWF antigen and activity, and genetic testing confirming the Type 2N mutation.

Record family history noting autosomal recessive inheritance pattern and any prior Hemophilia A diagnosis that should be revised.

MEAT Support

HCC Buddy guidance

Record family history noting autosomal recessive inheritance pattern and any prior Hemophilia A diagnosis that should be revised.

Audit Caution

HCC Buddy guidance

Frequently misdiagnosed as mild Hemophilia A because both present with reduced factor VIII.

The distinguishing test is the VWF:FVIII binding assay.

Female patients with low factor VIII should raise suspicion for Type 2N rather than Hemophilia A carrier status.

Update coding from D66 to D68.023 when the correct diagnosis is established.

Common Mistakes

HCC Buddy guidance

D66 (Hemophilia A) — most common misdiagnosis as both present with low factor VIII

D68.01 (Type 1) — may coexist with Type 2N as a compound heterozygote

D68.00 (Von Willebrand disease, unspecified) — use the specific Type 2N code when confirmed by VWF:FVIII binding assay.

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Is D68.023 an HCC code?

Yes. D68.023 (Von Willebrand disease, type 2N) maps to HCC 112, Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions under the CMS-HCC V28 risk adjustment model, with a source-labeled community non-dual aged reference coefficient of 0.450. Source-labeled code-level coefficients are references, not member totals. Actual contribution depends on complete member context, hierarchy and cleanup rules, interactions, and model year. HCC Buddy's RAF Calculator supports CMS-HCC V28 PY2026 and shows no score unless every required source and calculation check passes. It is billable for payment year 2026.

Coder answer: D68.023 is billable and maps to V28 HCC 112, Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions. Open it in the Code Book for the tabular path, RAF, and MEAT checklist.

Code: D68.023
Description: Von Willebrand disease, type 2N
HCC (V28): HCC 112 — Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions
RAF reference coefficient: 0.450
Billable: Yes
Payment year: 2026

HCC Category Mapping

V28HCC 112, Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions

0.450

ESRDHCC 48, Coagulation Defects and Other Specified Hematological Disorders

Not separately weighted

These are source-labeled model coefficients, not member totals. A category may still be removed by hierarchy or model cleanup rules. Weights are not directly comparable across models: CMS-HCC V28 and V24 use Community, Non-Dual, Aged; ESRD uses the dialysis continuing-enrollee model; RxHCC is the Part D continuing-enrollee, non-low-income, aged weight (a larger scale than CMS-HCC). ACA/HHS has no single weight — it varies by metal level. Actual per-patient RAF contribution depends on member context, hierarchy and cleanup rules, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains available for historical review.

Work D68.023 in the Code Book — tabular path, V28 RAF reference, and MEAT checklist →

MEAT Criteria for D68.023

For D68.023 to count as a valid HCC diagnosis in a given encounter, the provider's documentation must show MEAT: Monitor, Evaluate, Assess, or Treat. A diagnosis from a prior year does not carry forward automatically, it has to be re-documented and supported each calendar year.

MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
EEvaluate: test results, medication response, or physical findings reviewed by the provider
AAssess: explicit mention in the assessment or plan with acknowledgment of status
TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Only one of M/E/A/T is required to support the code, but the documentation must be specific enough to show that the provider actually addressed D68.023 during that encounter, not just copy-forwarded from a problem list.

Coder workflow notes

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What This Code Means

D68.023 is the ICD-10-CM diagnosis code for von willebrand disease, type 2n. Von Willebrand disease type 2N is a bleeding disorder where the body produces abnormal von Willebrand factor protein that doesn't work properly, causing difficulty with blood clotting and increased bleeding tendency. This specific type involves a defect in how the von Willebrand factor binds to platelets. D68.023 sits in the ICD-10-CM chapter for diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (d50-d89), within the section covering coagulation defects, purpura and other hemorrhagic conditions (d65-d69).

Under the CMS-HCC V28 risk adjustment model, D68.023 maps to Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions (HCC 112) with a source-labeled community, non-dual, aged reference coefficient of 0.450. No V24 mapping is shown for D68.023; use the applicable model and payment year when reviewing the V28 mapping. V28 is the CMS-HCC risk adjustment model that reached 100% phase-in for payment year 2026, replacing V24 which was used during the PY2024–PY2025 transition. Source-labeled code-level coefficients are references, not member totals. Actual contribution depends on complete member context, hierarchy and cleanup rules, interactions, and model year. HCC Buddy's RAF Calculator supports CMS-HCC V28 PY2026 and shows no score unless every required source and calculation check passes.

Verify the specific type of von Willebrand disease (type 1, 2A, 2B, 2M, 2N, or 3) is documented in the medical record before assigning this code, as each type has a distinct ICD-10-CM code. Because D68.023 maps to an HCC category, the provider's documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) before the diagnosis is used for risk adjustment. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.

HCC Buddy maintains structured V28 and V24 mapping, source-labeled coefficient references, and MEAT documentation criteria for D68.023 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

•Verify the specific type of von Willebrand disease (type 1, 2A, 2B, 2M, 2N, or 3) is documented in the medical record before assigning this code, as each type has a distinct ICD-10-CM code
•This code may be used alongside procedure codes for von Willebrand factor testing or treatment codes (such as desmopressin administration) depending on the clinical encounter

Clinical Significance

Von Willebrand disease type 2N (Normandy variant) is characterized by markedly reduced VWF binding affinity for factor VIII, resulting in accelerated factor VIII clearance and low factor VIII levels. This variant mimics mild Hemophilia A and may be misdiagnosed as such. Autosomal recessive inheritance distinguishes it from X-linked Hemophilia A.

Documentation Requirements

✓Document VWF:factor VIII binding assay results showing reduced binding capacity, low factor VIII levels with relatively normal VWF antigen and activity, and genetic testing confirming the Type 2N mutation.
✓Record family history noting autosomal recessive inheritance pattern and any prior Hemophilia A diagnosis that should be revised.

Commonly Confused Codes

•D66 (Hemophilia A): most common misdiagnosis as both present with low factor VIII
•D68.01 (Type 1): may coexist with Type 2N as a compound heterozygote
•D68.00 (Von Willebrand disease, unspecified): use the specific Type 2N code when confirmed by VWF:FVIII binding assay.