D58.8

HCC Category Mapping

What This Code Means

Other inherited blood disorders that cause red blood cells to break down prematurely, not classified in the more specific categories above.

Coding Tips

• •Use this code only when the specific hereditary hemolytic anemia type is documented but doesn't fit other D58 codes
• •Include documentation of the specific condition in the medical record

Clinical Significance

Other specified hereditary hemolytic anemias captures inherited conditions causing premature red blood cell destruction that do not fit into the more specific categories of spherocytosis, elliptocytosis, or hemoglobinopathies. This includes conditions such as stomatocytosis (hereditary hydrocytosis or xerocytosis), acanthocytosis from inherited membrane disorders, and other rare red blood cell enzyme or membrane defects. These conditions share the common feature of shortened red blood cell lifespan with compensatory increased marrow production.

Documentation Requirements

• ✓Document the specific hereditary hemolytic anemia by name when known.
• ✓Include peripheral blood smear findings showing the characteristic red blood cell morphology.
• ✓Record hemoglobin levels, reticulocyte count, and hemolysis markers (lactate dehydrogenase, indirect bilirubin, haptoglobin).
• ✓Document family history supporting hereditary etiology and any genetic testing results.
• ✓Note disease severity and current management approach.

Commonly Confused Codes