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D47.01 ICD-10-CM Code: Cutaneous mastocytosis

D47.01 is not a CMS-HCC payment code. MEAT criteria · RAF Calculator · HCC Buddy coding tools

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Code lookupD47.01

FY 2026 Apr update / Neoplasms (C00-D49) / Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes (D37-D48)

D47.01

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Cutaneous mastocytosis

An abnormal growth of mast cells limited to the skin, causing itching, flushing, or skin lesions.

Buddy the Bee presenting code insight

Buddy Insight

Cutaneous mastocytosis involves abnormal accumulation of mast cells limited to the skin, manifesting as urticaria pigmentosa, solitary mastocytoma, or diffuse cutaneous mastocytosis.

CMS-HCC V28

N/A

Not mapped

CMS-HCC V24

Historical

Historical

Not used for CY2026 payment

ACA/HHS

N/A

Not mapped

ESRD/PACE

N/A

Not mapped

RXHCC

HCC 21

Code-level coefficient reference

Inclusion Terms

Official
  • Diffuse cutaneous mastocytosis
  • Maculopapular cutaneous mastocytosis
  • Solitary mastocytoma
  • Telangiectasia macularis eruptiva perstans
  • Urticaria pigmentosa

Excludes 2

Official

No Excludes 2 notes are included in this display for D47.01. Check the code and parent instructions in the Code Book.

Includes

Official

No Includes notes are included in this display for D47.01. Check the code and parent instructions in the Code Book.

Excludes 1

Official
  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)
  • neoplasms of unspecified behavior (D49.-)Inherited from D37-D48, D47.0
  • congenital cutaneous mastocytosis (Q82.2)Inherited from D37-D48, D47.0
  • histiocytic neoplasms of uncertain behavior (D47.Z9)Inherited from D37-D48, D47.0
  • malignant mast cell neoplasm (C96.2-)Inherited from D37-D48, D47.0

Code First

Official

No Code First sequencing instructions are included in this display for D47.01. Check the code and parent instructions in the Code Book.

Use Additional

Official

No Use Additional Code instructions are included in this display for D47.01. Check the code and parent instructions in the Code Book.

Code Also

Official

No Code Also instructions are included in this display for D47.01. Check the code and parent instructions in the Code Book.

Buddy Documentation Tip

HCC Buddy guidance
Documentation should confirm cutaneous-only involvement with no systemic disease, supported by skin biopsy showing mast cell infiltration.
Tryptase levels should be documented to help exclude systemic disease.
Describe the skin lesion morphology, distribution, and any symptoms related to mast cell degranulation.
Darier sign (urtication upon rubbing) should be noted if present.

MEAT Support

HCC Buddy guidance
Documentation should confirm cutaneous-only involvement with no systemic disease, supported by skin biopsy showing mast cell infiltration.
Tryptase levels should be documented to help exclude systemic disease.
Describe the skin lesion morphology, distribution, and any symptoms related to mast cell degranulation.
Darier sign (urtication upon rubbing) should be noted if present.

Audit Caution

HCC Buddy guidance
Ensure systemic involvement has been excluded before assigning cutaneous mastocytosis
serum tryptase levels and bone marrow biopsy may be needed to rule out systemic disease. Pediatric cutaneous mastocytosis often resolves and should not be coded as systemic unless documented. Do not confuse with chronic urticaria or other allergic skin conditions.

Common Mistakes

HCC Buddy guidance
D47.02 (systemic mastocytosis) involves extracutaneous organ involvement and requires different management.
D47.09 (other mast cell neoplasms) covers other mast cell tumors not fitting cutaneous or systemic categories.
L50.0 (allergic urticaria) may present similarly but lacks mast cell clonal proliferation.
C96.20 (malignant mast cell neoplasm) is used for mast cell leukemia or sarcoma.

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Is D47.01 an HCC code?

D47.01 is not in the CMS-HCC V28 or V24 community payment model. D47.01 has a separate mapping under the Part D RxHCC model (HCC 21 (Lymphomas and Other Hematologic Cancers)); the applicable result needs member context.

Code
D47.01
Description
Cutaneous mastocytosis
HCC (V28)
No CMS-HCC V28 mapping
RAF reference coefficient
Billable
Yes
Payment year
2026

HCC Category Mapping

RxHCCHCC 21, Lymphomas and Other Hematologic Cancers
Not separately weighted

These are source-labeled model coefficients, not member totals. A category may still be removed by hierarchy or model cleanup rules. Weights are not directly comparable across models: CMS-HCC V28 and V24 use Community, Non-Dual, Aged; ESRD uses the dialysis continuing-enrollee model; RxHCC is the Part D continuing-enrollee, non-low-income, aged weight (a larger scale than CMS-HCC). ACA/HHS has no single weight — it varies by metal level. Actual per-patient RAF contribution depends on member context, hierarchy and cleanup rules, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains available for historical review.

Work D47.01 in the Code Book — tabular path, V28 RAF reference, and MEAT checklist →

MEAT review for D47.01

For D47.01, confirm that the documentation supports the diagnosis and meets the applicable coding, encounter, program and payer requirements. MEAT (Monitor, Evaluate, Assess, or Treat) is a review mnemonic, not a universal CMS coding rule.

  • MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
  • EEvaluate: test results, medication response, or physical findings reviewed by the provider
  • AAssess: explicit mention in the assessment or plan with acknowledgment of status
  • TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Coder workflow notes

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What This Code Means

D47.01 is the ICD-10-CM diagnosis code for cutaneous mastocytosis. An abnormal growth of mast cells limited to the skin, causing itching, flushing, or skin lesions. D47.01 sits in the ICD-10-CM chapter for neoplasms (c00-d49), within the section covering neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes (d37-d48).

D47.01 has no mapping under the CMS-HCC V28 or V24 community payment models. D47.01 has a separate mapping under the Part D RxHCC model (HCC 21 (Lymphomas and Other Hematologic Cancers)); the applicable result needs member context. Do not assign V28 risk adjustment value from this page; verify the applicable model and payment year before using this code for risk adjustment.

Confirm diagnosis is limited to skin involvement; systemic involvement would require code D47.02.

HCC Buddy maintains structured V28 and V24 mapping, source-labeled coefficient references, and MEAT documentation criteria for D47.01 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • Confirm diagnosis is limited to skin involvement; systemic involvement would require code D47.02
  • Document skin manifestations and any biopsy confirmation of mast cell infiltration

Clinical Significance

Cutaneous mastocytosis involves abnormal accumulation of mast cells limited to the skin, manifesting as urticaria pigmentosa, solitary mastocytoma, or diffuse cutaneous mastocytosis. While primarily a skin disease, it can cause significant symptoms from mast cell mediator release including flushing, pruritus, and blistering, particularly in pediatric patients where it often resolves spontaneously.

Documentation Requirements

  • Documentation should confirm cutaneous-only involvement with no systemic disease, supported by skin biopsy showing mast cell infiltration.
  • Tryptase levels should be documented to help exclude systemic disease.
  • Describe the skin lesion morphology, distribution, and any symptoms related to mast cell degranulation.
  • Darier sign (urtication upon rubbing) should be noted if present.

Excludes 1, Do NOT code together

  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)

Commonly Confused Codes

  • D47.02 (systemic mastocytosis) involves extracutaneous organ involvement and requires different management.
  • D47.09 (other mast cell neoplasms) covers other mast cell tumors not fitting cutaneous or systemic categories.
  • L50.0 (allergic urticaria) may present similarly but lacks mast cell clonal proliferation.
  • C96.20 (malignant mast cell neoplasm) is used for mast cell leukemia or sarcoma.

Child Codes

Code Hierarchy

D47.01 code history

Code setChange
FY2018 (effective Oct 1, 2017)Added to the code set

Source: official CMS ICD-10-CM order and addenda files, FY2016 through FY2027.

Also searched as

  • D47 01
  • D4701

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