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C84.73

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Anaplastic large cell lymphoma, ALK-negative, intra-abdominal lymph nodes

HCC Category Mapping

V28HCC 19Lymphoma and Other Cancers
0.105
V24HCC 10Lymphoma and Other Cancers
0.675
ESRDHCC 10Lymphoma and Other Cancers
0.000
RxHCCHCC 21Hodgkin Lymphoma and Other Cancers
0.000

What This Code Means

A type of aggressive lymphoma (cancer of immune cells) without a specific genetic marker (ALK-negative) that is located in the lymph nodes within the abdominal cavity.

Coding Tips

  • Verify specific abdominal lymph node involvement (mesenteric, retroperitoneal, etc.) through imaging or pathology reports
  • Distinguish from splenic involvement, which has a separate code (C84.77)

Clinical Significance

Anaplastic large cell lymphoma, ALK-negative, involving intra-abdominal lymph nodes indicates aggressive T-cell lymphoma without the ALK marker affecting abdominal nodal basins. Abdominal ALCL may present with nonspecific symptoms such as pain, bloating, or weight loss. The worse prognosis of ALK-negative disease necessitates aggressive multiagent chemotherapy.

Documentation Requirements

  • Pathology confirming ALCL with ALK-negative status
  • Abdominal imaging documenting specific lymph node groups involved
  • CD30 positivity and T-cell markers on immunohistochemistry
  • Distinction from hepatosplenic T-cell lymphoma and enteropathy-associated T-cell lymphoma
  • Clinical staging documentation

Commonly Confused Codes

Code Hierarchy

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