C84.63
BillableAnaplastic large cell lymphoma, ALK-positive, intra-abdominal lymph nodes
HCC Category Mapping
V28HCC 20 — Lung and Other Severe Cancers
0.000V24HCC 10 — Lymphoma and Other Cancers
0.675ESRDHCC 10 — Lymphoma and Other Cancers
0.000RxHCCHCC 21 — Hodgkin Lymphoma and Other Cancers
0.000What This Code Means
An aggressive type of lymphoma with large abnormal cells that is positive for ALK protein, affecting lymph nodes in the abdomen.
Coding Tips
- •Ensure ALK-positive status is confirmed in pathology report
- •Document that intra-abdominal lymph nodes are involved, not other abdominal organs
Clinical Significance
Anaplastic large cell lymphoma, ALK-positive, involving intra-abdominal lymph nodes indicates abdominal nodal disease from an ALK-driven T-cell malignancy. Abdominal ALCL can involve mesenteric, retroperitoneal, and para-aortic nodes, potentially causing bowel obstruction or obstructive uropathy. The ALK-positive status provides therapeutic targets and generally better outcomes.
Documentation Requirements
- ✓Pathology confirming ALCL with ALK positivity
- ✓Abdominal imaging documenting specific lymph node groups involved
- ✓CD30 positivity on immunohistochemistry
- ✓T-cell lineage confirmed
- ✓Clinical stage with specific abdominal findings
Commonly Confused Codes
C84.73 — ALCL, ALK-negative, intra-abdominal: Different ALK status; verify molecular resultsC84.43 — PTCL-NOS, intra-abdominal: Different lymphoma subtype; ALCL has distinct morphologyC84.66 — ALCL ALK-positive, intrapelvic: Intrapelvic nodes are below the pelvic brim, distinct from intra-abdominalC86.2 — Enteropathy-associated T-cell lymphoma: Specific intestinal T-cell lymphoma, not ALCL
Code Hierarchy
└C84Mature T/NK-cell lymphomas└C84.6Anaplastic large cell lymphoma, ALK-positive└C84.63Anaplastic large cell lymphoma, ALK-positive, intra-abdominal lymph nodes
└C84.63Anaplastic large cell lymphoma, ALK-positive, intra-abdominal lymph nodes