C84.19
BillableSézary disease, extranodal and solid organ sites
HCC Category Mapping
V28HCC 17 — Metastatic Cancer and Acute Leukemia
0.368V24HCC 10 — Lymphoma and Other Cancers
0.675ESRDHCC 10 — Lymphoma and Other Cancers
0.000RxHCCHCC 19 — Lymphoma and Other Cancers
0.000What This Code Means
Sézary disease affecting organs and tissues outside the lymph node system, such as the liver, lungs, or other solid organs.
Coding Tips
- •Use this code when Sézary disease involves extranodal sites or solid organs rather than lymph nodes
- •Document the specific extranodal sites involved for clinical clarity
Clinical Significance
Sezary disease with extranodal and solid organ involvement represents the most advanced form of this leukemic T-cell lymphoma with spread beyond the skin, blood, and lymph nodes into visceral organs. This may include liver, lung, bone marrow, or gastrointestinal involvement and carries the worst prognosis among Sezary disease presentations, often indicating transformation or treatment-refractory disease.
Documentation Requirements
- ✓Peripheral blood demonstrating circulating Sezary cells
- ✓Documentation of specific extranodal organs involved
- ✓Imaging or biopsy confirming organ involvement
- ✓Assessment for large cell transformation
- ✓TNMB staging and intensive treatment plan
Commonly Confused Codes
C84.18 — Sezary disease, multiple sites: C84.18 is for multiple lymph node sites; C84.19 is for non-nodal organ involvementC84.17 — Sezary disease, spleen: Splenic involvement has its own code; use C84.19 for other organ involvementC78-C79 — Secondary malignant neoplasms: Do not use metastasis codes for Sezary disease organ involvement
Code Hierarchy
└C84Mature T/NK-cell lymphomas└C84.1Sézary disease└C84.19Sézary disease, extranodal and solid organ sites
└C84.19Sézary disease, extranodal and solid organ sites