C84.16
BillableSézary disease, intrapelvic lymph nodes
HCC Category Mapping
V28HCC 17 — Metastatic Cancer and Acute Leukemia
0.368V24HCC 10 — Lymphoma and Other Cancers
0.675ESRDHCC 10 — Lymphoma and Other Cancers
0.000RxHCCHCC 19 — Lymphoma and Other Cancers
0.000What This Code Means
Sézary disease, an aggressive form of skin cancer, affecting lymph nodes inside the pelvis.
Coding Tips
- •Confirm intrapelvic lymph node involvement through imaging or pathology reports
- •This includes iliac, obturator, and other pelvic lymph nodes
Clinical Significance
Sezary disease with intrapelvic lymph node involvement indicates deep pelvic lymph node spread in this aggressive leukemic T-cell lymphoma. Intrapelvic involvement is relatively uncommon and represents significant visceral lymph node disease requiring systemic management. This finding typically contributes to advanced disease staging.
Documentation Requirements
- ✓Peripheral blood demonstrating circulating Sezary cells
- ✓Pelvic imaging documenting intrapelvic lymphadenopathy
- ✓Skin biopsy confirming cutaneous T-cell lymphoma
- ✓TNMB staging reflecting deep nodal disease
- ✓Systemic treatment plan
Commonly Confused Codes
Code Hierarchy
└C84Mature T/NK-cell lymphomas└C84.1Sézary disease└C84.16Sézary disease, intrapelvic lymph nodes
└C84.16Sézary disease, intrapelvic lymph nodes