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C84.13

Billable

Sézary disease, intra-abdominal lymph nodes

HCC Category Mapping

V28HCC 17Metastatic Cancer and Acute Leukemia
0.368
V24HCC 10Lymphoma and Other Cancers
0.675
ESRDHCC 10Lymphoma and Other Cancers
0.000
RxHCCHCC 19Lymphoma and Other Cancers
0.000

What This Code Means

Sézary disease, an aggressive form of skin cancer, affecting lymph nodes in the abdominal cavity.

Coding Tips

  • Verify documentation confirms intra-abdominal lymph node involvement
  • This includes mesenteric, retroperitoneal, and other abdominal lymph nodes

Clinical Significance

Sezary disease with intra-abdominal lymph node involvement indicates spread to mesenteric, retroperitoneal, or other abdominal lymph nodes in this aggressive leukemic cutaneous T-cell lymphoma. Abdominal lymphadenopathy may cause gastrointestinal symptoms and indicates extensive systemic disease requiring aggressive therapy.

Documentation Requirements

  • Peripheral blood demonstrating circulating Sezary cells
  • Abdominal imaging documenting intra-abdominal lymphadenopathy
  • Skin biopsy confirming cutaneous T-cell lymphoma
  • TNMB staging reflecting abdominal nodal disease
  • Treatment plan addressing systemic disease

Commonly Confused Codes

Code Hierarchy

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