C84.13
BillableSézary disease, intra-abdominal lymph nodes
HCC Category Mapping
V28HCC 17 — Metastatic Cancer and Acute Leukemia
0.368V24HCC 10 — Lymphoma and Other Cancers
0.675ESRDHCC 10 — Lymphoma and Other Cancers
0.000RxHCCHCC 19 — Lymphoma and Other Cancers
0.000What This Code Means
Sézary disease, an aggressive form of skin cancer, affecting lymph nodes in the abdominal cavity.
Coding Tips
- •Verify documentation confirms intra-abdominal lymph node involvement
- •This includes mesenteric, retroperitoneal, and other abdominal lymph nodes
Clinical Significance
Sezary disease with intra-abdominal lymph node involvement indicates spread to mesenteric, retroperitoneal, or other abdominal lymph nodes in this aggressive leukemic cutaneous T-cell lymphoma. Abdominal lymphadenopathy may cause gastrointestinal symptoms and indicates extensive systemic disease requiring aggressive therapy.
Documentation Requirements
- ✓Peripheral blood demonstrating circulating Sezary cells
- ✓Abdominal imaging documenting intra-abdominal lymphadenopathy
- ✓Skin biopsy confirming cutaneous T-cell lymphoma
- ✓TNMB staging reflecting abdominal nodal disease
- ✓Treatment plan addressing systemic disease
Commonly Confused Codes
Code Hierarchy
└C84Mature T/NK-cell lymphomas└C84.1Sézary disease└C84.13Sézary disease, intra-abdominal lymph nodes
└C84.13Sézary disease, intra-abdominal lymph nodes