C84.12
BillableSézary disease, intrathoracic lymph nodes
HCC Category Mapping
V28HCC 17 — Metastatic Cancer and Acute Leukemia
0.368V24HCC 10 — Lymphoma and Other Cancers
0.675ESRDHCC 10 — Lymphoma and Other Cancers
0.000RxHCCHCC 19 — Lymphoma and Other Cancers
0.000What This Code Means
Sézary disease, an aggressive form of skin cancer, affecting lymph nodes inside the chest cavity.
Coding Tips
- •Confirm intrathoracic lymph node involvement through imaging or pathology documentation
- •This code indicates mediastinal and/or hilar lymph node involvement
Clinical Significance
Sezary disease with intrathoracic lymph node involvement indicates spread to mediastinal or hilar lymph nodes in this aggressive leukemic T-cell lymphoma. Intrathoracic involvement may cause respiratory symptoms and represents extensive disease requiring systemic management. This is an expected finding in advanced Sezary disease.
Documentation Requirements
- ✓Peripheral blood demonstrating circulating Sezary cells
- ✓Chest imaging documenting intrathoracic lymphadenopathy
- ✓Skin biopsy confirming cutaneous T-cell lymphoma
- ✓TNMB staging
- ✓Systemic treatment plan
Commonly Confused Codes
Code Hierarchy
└C84Mature T/NK-cell lymphomas└C84.1Sézary disease└C84.12Sézary disease, intrathoracic lymph nodes
└C84.12Sézary disease, intrathoracic lymph nodes