C83.59
BillableLymphoblastic (diffuse) lymphoma, extranodal and solid organ sites
HCC Category Mapping
V28HCC 20 — Lung and Other Severe Cancers
0.000V24HCC 10 — Lymphoma and Other Cancers
0.675ESRDHCC 10 — Lymphoma and Other Cancers
0.000RxHCCHCC 21 — Hodgkin Lymphoma and Other Cancers
0.000What This Code Means
A type of blood cancer (lymphoblastic lymphoma) that has spread to organs outside the lymph node system, such as the liver, lungs, or other solid organs.
Coding Tips
- •This code requires documentation of the specific extranodal or solid organ site involved; review pathology reports for site confirmation
- •Do not use this code if the lymphoma is limited to lymph nodes; verify extranodal involvement is documented
Clinical Significance
Lymphoblastic lymphoma of extranodal and solid organ sites indicates disease involvement beyond the lymph node system, which may include bone marrow (below leukemia threshold), liver, skin, gonads, or other organs. Extranodal involvement often indicates more advanced disease and may require modification of treatment intensity.
Documentation Requirements
- ✓Pathology confirmation from the specific extranodal site with TdT staining
- ✓Documentation of specific organ(s) involved
- ✓Bone marrow biopsy with blast percentage documented (must be <25% for lymphoma designation)
- ✓Imaging confirming extranodal involvement
- ✓CNS evaluation for occult involvement
Commonly Confused Codes
C83.57 — Lymphoblastic lymphoma, spleen; splenic involvement has its own specific codeC83.58 — Multiple nodal sites; C83.59 is for non-nodal organ involvementC91.00 — Acute lymphoblastic leukemia; bone marrow blasts >25% means leukemia, not extranodal lymphomaC83.398 — DLBCL, extranodal; mature vs. immature cell distinction
Code Hierarchy
└C83Non-follicular lymphoma└C83.5Lymphoblastic (diffuse) lymphoma└C83.59Lymphoblastic (diffuse) lymphoma, extranodal and solid organ sites
└C83.59Lymphoblastic (diffuse) lymphoma, extranodal and solid organ sites