C83.19
BillableMantle cell lymphoma, extranodal and solid organ sites
HCC Category Mapping
V28HCC 20 — Lung and Other Severe Cancers
0.000V24HCC 10 — Lymphoma and Other Cancers
0.675ESRDHCC 10 — Lymphoma and Other Cancers
0.000RxHCCHCC 19 — Lymphoma and Other Cancers
0.000What This Code Means
A type of cancer affecting B-cells that has spread to organs or tissues outside the lymph node system.
Coding Tips
- •Document specific extranodal sites involved (e.g., liver, bone, GI tract, bone marrow)
- •This indicates more advanced mantle cell lymphoma; ensure staging is documented
Clinical Significance
Mantle cell lymphoma of extranodal and solid organ sites is clinically important because mantle cell lymphoma has a distinctive predilection for the gastrointestinal tract, presenting as lymphomatoid polyposis. Up to 90% of patients have GI involvement when endoscopy is performed. Other extranodal sites include bone marrow, liver, and Waldeyer ring.
Documentation Requirements
- ✓Pathology confirmation from the specific extranodal site
- ✓Documentation of specific organ(s) involved (GI tract, bone marrow, liver, etc.)
- ✓Endoscopy/colonoscopy results if GI involvement suspected (lymphomatoid polyposis)
- ✓Bone marrow biopsy results
- ✓Imaging confirming extranodal involvement
Commonly Confused Codes
C83.17 — Mantle cell lymphoma, spleen; splenic involvement has its own codeC83.18 — Multiple lymph node sites; C83.19 is for non-nodal organ involvementC83.13 — Intra-abdominal lymph nodes; GI mucosal involvement is extranodal, not nodalC83.09 — Small cell B-cell lymphoma, extranodal; different histological subtype
Code Hierarchy
└C83Non-follicular lymphoma└C83.1Mantle cell lymphoma└C83.19Mantle cell lymphoma, extranodal and solid organ sites
└C83.19Mantle cell lymphoma, extranodal and solid organ sites