Skip to content

A50.54 ICD-10-CM Code: Late congenital cardiovascular syphilis

A50.54 is not a CMS-HCC payment code. MEAT criteria · RAF calculator · free HCC coding tools

ICD-10-CM Code View

HCC Buddy Code Card

Digital ICD-10 code-book layout with official code detail, always-visible risk models, Code Trumping, and Buddy coding guidance.

FY 2026 Apr update / Certain infectious and parasitic diseases (A00-B99) / Infections with a predominantly sexual mode of transmission (A50-A64)

A50.54

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Late congenital cardiovascular syphilis

This is a heart and blood vessel infection caused by syphilis that was passed from mother to baby before birth and is now showing up later in childhood or adulthood. The infection damages the heart structures and major blood vessels.

CMS-HCC V28

N/A

Not mapped

CMS-HCC V24

N/A

Not mapped

ACA/HHS

HCC 135

Varies by metal level

ESRD/PACE

N/A

Not mapped

RXHCC

N/A

Not mapped

Code Book Path

Official
A50Congenital syphilis
A50.5Other late congenital syphilis, symptomatic
A50.54Late congenital cardiovascular syphilis

Inclusion Terms

Official
  • Any congenital syphilitic condition specified as late or manifest two years or more after birth.

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for A50.54 in this effective period.

Related Child Codes

Official
A50.51Clutton's joints
A50.52Hutchinson's teeth
A50.53Hutchinson's triad
A50.55Late congenital syphilitic arthropathy
A50.56Late congenital syphilitic osteochondropathy

Includes

Official

ICD-10-CM does not list Includes notes for A50.54 in this effective period.

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for A50.54 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for A50.54 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for A50.54 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for A50.54 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance
This code is used only for cardiovascular manifestations of late congenital syphilis (typically appearing after age 2); ensure the syphilis is confirmed as congenital and not acquired
Do not use this code for early congenital syphilis (before age 2) or for acquired syphilis; verify documentation clearly states 'late congenital' and specifies cardiovascular involvement

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Is A50.54 an HCC code?

No. A50.54 is a billable ICD-10-CM code but does not map to any HCC category in V28, V24, ESRD, or RxHCC.

Code
A50.54
Description
Late congenital cardiovascular syphilis
HCC (V28)
No CMS-HCC V28 mapping
RAF
Billable
Yes
Payment year
2026

Coder workflow notes

Get the V28 RAF + MEAT cheat sheet

One printable page: confirm a code's V28 HCC status, its RAF weight, and the MEAT your note needs to make it stick. Free, no card.

Free PDF. No card. Unsubscribe anytime.

This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).

What This Code Means

A50.54 is the ICD-10-CM diagnosis code for late congenital cardiovascular syphilis. This is a heart and blood vessel infection caused by syphilis that was passed from mother to baby before birth and is now showing up later in childhood or adulthood. The infection damages the heart structures and major blood vessels. A50.54 sits in the ICD-10-CM chapter for certain infectious and parasitic diseases (a00-b99), within the section covering infections with a predominantly sexual mode of transmission (a50-a64).

A50.54 is a billable ICD-10-CM code but does not map to a payment HCC under the CMS-HCC V28, V24, ESRD, or RxHCC risk adjustment models. It can be reported on Medicare Advantage encounter data submissions but it does not contribute to a beneficiary's RAF score and therefore does not affect risk-adjusted payments to the plan.

This code is used only for cardiovascular manifestations of late congenital syphilis (typically appearing after age 2); ensure the syphilis is confirmed as congenital and not acquired.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for A50.54 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • This code is used only for cardiovascular manifestations of late congenital syphilis (typically appearing after age 2); ensure the syphilis is confirmed as congenital and not acquired
  • Do not use this code for early congenital syphilis (before age 2) or for acquired syphilis; verify documentation clearly states 'late congenital' and specifies cardiovascular involvement

Child Codes

Code Hierarchy

Work A50.54 in HCC Buddy

Open A50.54 in the Code Book for the full Index-to-Tabular path, MEAT checklist, and V28 HCC mapping, or in the Encoder to code from a keyword search. Pro includes 7 days to try everything, no card required.