Q85.02

Billable

Neurofibromatosis, type 2

HCC Category Mapping

V28HCC 23 — Melanoma and Other Skin Cancers

0.251

V24HCC 12 — Breast, Prostate, and Other Cancers and Tumors

0.150

ESRDHCC 12 — Breast, Prostate, and Other Cancers and Tumors

0.000

What This Code Means

Neurofibromatosis type 2 is an inherited genetic disorder characterized by benign tumors on the hearing nerves and other nerve tissues, often causing hearing loss.

Coding Tips

•NF2 typically presents with bilateral acoustic neuromas; document hearing loss and other neurological manifestations
•Link this code with codes for associated conditions like hearing impairment or neurological complications

Clinical Significance

Neurofibromatosis type 2 is a rare but serious genetic disorder characterized by bilateral acoustic neuromas with high risk of hearing loss and other central nervous system tumors, requiring specialized neurosurgical and audiological management. The condition often presents in young adults and can be life-altering, making early diagnosis and intervention crucial for preserving function.

Documentation Requirements

✓Bilateral vestibular schwannomas (acoustic neuromas)
✓Unilateral vestibular schwannoma plus family history of NF2
✓Multiple meningiomas plus unilateral vestibular schwannoma
✓Genetic testing confirming NF2 gene mutation
✓Audiological assessment documentation
✓MRI findings of central nervous system tumors
✓Family history and genetic counseling records

Commonly Confused Codes

Q85.01 — NF1 (peripheral manifestations, different gene)Q85.03 — Schwannomatosis (no bilateral acoustic neuromas)D33.3 — Benign neoplasm of acoustic nerve (individual tumor)H93.3 — Disorders of acoustic nerve (hearing loss symptom)