J84.178
BillableOther interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
HCC Category Mapping
V28HCC 280 — Chronic Obstructive Pulmonary Disease
0.334V24HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
0.268ESRDHCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
0.000RxHCCHCC 227 — Sarcoidosis, Pulmonary Alveolar Disorders
0.000What This Code Means
Scarring and inflammation of lung tissue that occurs as a complication of another disease, affecting the lung's ability to function properly.
Coding Tips
- •Requires documentation of the primary disease causing the interstitial lung disease
- •Use when fibrosis is present but does not fit other more specific J84.17x codes
Clinical Significance
Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere captures fibrotic ILD manifestations of systemic diseases that do not meet the progressive fibrotic phenotype criteria. This secondary diagnosis code reflects the pulmonary fibrotic burden in patients with conditions like connective tissue diseases, sarcoidosis, or other systemic conditions affecting the lungs.
Documentation Requirements
- ✓Documentation of the underlying disease classified elsewhere causing the interstitial lung disease with fibrosis
- ✓Imaging evidence of fibrosis (high-resolution computed tomography showing reticular changes, honeycombing, or traction bronchiectasis)
- ✓Pulmonary function test results documenting the fibrotic impact
- ✓Documentation that the fibrosis is NOT progressive (if progressive, use J84.170 instead)
- ✓Code the underlying disease first, with this as a secondary/manifestation code
Code First
Commonly Confused Codes
J84.170 — Interstitial lung disease with progressive fibrotic phenotype is used when there is documented progressive fibrotic decline — carries much higher HCC weight in V28J84.112 — Idiopathic pulmonary fibrosis is a primary diagnosis, not a manifestation of another diseaseJ84.10 — Pulmonary fibrosis unspecified does not capture the relationship to an underlying classified diseaseJ84.89 — Other specified interstitial pulmonary diseases does not specify the fibrotic component in a classified disease
Code Hierarchy
└J84Other interstitial pulmonary diseases└J84.1Other interstitial pulmonary diseases with fibrosis└J84.17Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere└J84.178Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
└J84.178Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere