J84.02
BillablePulmonary alveolar microlithiasis
HCC Category Mapping
V28HCC 280 — Chronic Obstructive Pulmonary Disease
0.334V24HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
0.268ESRDHCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
0.000RxHCCHCC 227 — Sarcoidosis, Pulmonary Alveolar Disorders
0.000What This Code Means
A rare inherited lung disease where tiny mineral deposits accumulate in the lungs, causing progressive breathing problems.
Coding Tips
- •This is a genetic condition; document family history if available
- •Verify imaging findings support the diagnosis of microlithiasis
Clinical Significance
Pulmonary alveolar microlithiasis is a rare genetic lung disease characterized by progressive intra-alveolar calcium phosphate microliths. It is significant for risk adjustment because it can progress to respiratory failure over years to decades, requiring long-term monitoring, and in severe cases, lung transplantation evaluation.
Documentation Requirements
- ✓Chest imaging showing characteristic 'sandstorm' appearance with diffuse bilateral calcifications
- ✓Family history of pulmonary alveolar microlithiasis (autosomal recessive inheritance, SLC34A2 gene mutations)
- ✓Pulmonary function test results documenting restrictive defect progression
- ✓Clinical assessment of disease severity and oxygen requirements
- ✓Genetic testing results if performed
- ✓Treatment plan and transplant evaluation status if applicable
Commonly Confused Codes
J84.01 (Alveolar proteinosis) — proteinaceous material vs. mineral deposits in alveoliJ84.10 (Pulmonary fibrosis, unspecified) — microlithiasis is not primarily fibroticJ63.4 (Siderosis) — iron deposits from occupational exposure vs. calcium phosphate deposits from genetic diseaseJ84.09 (Other alveolar and parieto-alveolar conditions) — use J84.02 specifically for microlithiasis
Code Hierarchy
└J84Other interstitial pulmonary diseases└J84.0Alveolar and parieto-alveolar conditions└J84.02Pulmonary alveolar microlithiasis
└J84.02Pulmonary alveolar microlithiasis