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H35.54 ICD-10-CM Code: Dystrophies primarily involving the retinal pigment epithelium

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FY 2026 Apr update / Diseases of the eye and adnexa (H00-H59) / Disorders of choroid and retina (H30-H36)

H35.54

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Dystrophies primarily involving the retinal pigment epithelium

A hereditary condition causing progressive degeneration of the retinal pigment epithelium, which is the layer of cells that supports and nourishes the light-sensitive tissue of the eye.

CMS-HCC V28

0

0

RAF 0

CMS-HCC V24

0

0

RAF 0

ACA/HHS

0

0

RAF 0

ESRD/PACE

0

0

RAF 0

RXHCC

0

0

RAF 0

Code Trumping

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Code Book Path

Official
H35Other retinal disorders
H35.5Hereditary retinal dystrophy
H35.54Dystrophies primarily involving the retinal pigment epithelium

Inclusion Terms

Official
  • Vitelliform retinal dystrophy

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for H35.54 in this effective period.

Related Child Codes

Official
H35.50Unspecified hereditary retinal dystrophy
H35.51Vitreoretinal dystrophy
H35.52Pigmentary retinal dystrophy
H35.53Other dystrophies primarily involving the sensory retina

Includes

Official

ICD-10-CM does not list Includes notes for H35.54 in this effective period.

Excludes 1

Official
  • dystrophies primarily involving Bruch's membrane (H31.1-)

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for H35.54 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for H35.54 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for H35.54 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance
This code specifically indicates primary involvement of the retinal pigment epithelium layer, not the sensory retina itself
Differentiate from H35.53, which affects the sensory retina rather than the pigment epithelium

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Is H35.54 an HCC code?

No. H35.54 is a billable ICD-10-CM code but does not map to any HCC category in V28, V24, ESRD, or RxHCC.

This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).

What This Code Means

H35.54 is the ICD-10-CM diagnosis code for dystrophies primarily involving the retinal pigment epithelium. A hereditary condition causing progressive degeneration of the retinal pigment epithelium, which is the layer of cells that supports and nourishes the light-sensitive tissue of the eye. H35.54 sits in the ICD-10-CM chapter for diseases of the eye and adnexa (h00-h59), within the section covering disorders of choroid and retina (h30-h36).

H35.54 is a billable ICD-10-CM code but does not map to a payment HCC under the CMS-HCC V28, V24, ESRD, or RxHCC risk adjustment models. It can be reported on Medicare Advantage encounter data submissions but it does not contribute to a beneficiary's RAF score and therefore does not affect risk-adjusted payments to the plan.

This code specifically indicates primary involvement of the retinal pigment epithelium layer, not the sensory retina itself.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for H35.54 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • This code specifically indicates primary involvement of the retinal pigment epithelium layer, not the sensory retina itself
  • Differentiate from H35.53, which affects the sensory retina rather than the pigment epithelium

Child Codes

Code Hierarchy

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