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C84.09

Billable

Mycosis fungoides, extranodal and solid organ sites

HCC Category Mapping

V28HCC 20Lung and Other Severe Cancers
0.000
V24HCC 10Lymphoma and Other Cancers
0.675
ESRDHCC 10Lymphoma and Other Cancers
0.000
RxHCCHCC 19Lymphoma and Other Cancers
0.000

What This Code Means

A type of skin cancer (mycosis fungoides) that has spread to organs or tissues outside the lymph node system.

Coding Tips

  • This code captures extranodal involvement; document which specific organs or tissues are affected
  • Distinguish from nodal involvement codes to ensure accurate staging and prognosis assessment

Clinical Significance

Mycosis fungoides with extranodal and solid organ involvement represents the most advanced form of cutaneous T-cell lymphoma with spread to visceral organs beyond the skin and lymph nodes. This may include liver, lung, bone marrow, or gastrointestinal involvement. Extranodal mycosis fungoides carries a very poor prognosis and often indicates large cell transformation requiring aggressive systemic therapy.

Documentation Requirements

  • Skin biopsy confirming mycosis fungoides
  • Documentation of specific extranodal organs involved
  • Imaging or biopsy confirming organ involvement
  • Assessment for large cell transformation
  • TNMB staging reflecting visceral involvement and treatment plan

Commonly Confused Codes

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