C84.02
BillableMycosis fungoides, intrathoracic lymph nodes
HCC Category Mapping
V28HCC 20 — Lung and Other Severe Cancers
0.000V24HCC 10 — Lymphoma and Other Cancers
0.675ESRDHCC 10 — Lymphoma and Other Cancers
0.000RxHCCHCC 19 — Lymphoma and Other Cancers
0.000What This Code Means
A rare type of skin cancer (mycosis fungoides) that has spread to the lymph nodes inside the chest.
Coding Tips
- •Confirm intrathoracic lymph node involvement through CT chest imaging
- •The '2' designator indicates mediastinal and hilar lymph node involvement
Clinical Significance
Mycosis fungoides with intrathoracic lymph node involvement indicates advanced disease with spread to mediastinal or hilar lymph nodes. This is uncommon in mycosis fungoides and represents significant disease progression requiring systemic treatment. Intrathoracic involvement is typically detected on staging CT or PET/CT scans.
Documentation Requirements
- ✓Skin biopsy confirming mycosis fungoides diagnosis
- ✓Chest imaging (CT or PET/CT) documenting intrathoracic lymphadenopathy
- ✓Pathologic confirmation of lymphomatous involvement if biopsy performed
- ✓TNMB staging reflecting intrathoracic nodal disease
- ✓Systemic treatment plan
Commonly Confused Codes
C84.00 — Mycosis fungoides, unspecified site: Use C84.02 when intrathoracic lymph node involvement is confirmedC84.12 — Sezary disease, intrathoracic: Distinct diagnosis; Sezary disease requires circulating malignant T-cellsC83.92 — Non-follicular lymphoma, unspecified, intrathoracic: Use for non-follicular lymphoma, not mycosis fungoides