C81.40

HCC Category Mapping

What This Code Means

A rare type of Hodgkin lymphoma (lymphocyte-rich variant) with an unspecified location of involvement.

Coding Tips

• •Use this code only when the specific site of lymphoma involvement is not documented
• •Query the provider if site information is available to assign a more specific code

Clinical Significance

Lymphocyte-rich Hodgkin lymphoma is a relatively uncommon subtype of classical Hodgkin lymphoma with the most favorable prognosis among all Hodgkin subtypes, often presenting at an early stage. The unspecified site designation means the anatomic location was not documented. Despite its indolent behavior, these patients require ongoing monitoring and treatment, and the code is important for risk adjustment capture.

Documentation Requirements

• ✓Pathology confirming lymphocyte-rich classical Hodgkin lymphoma (distinct from nodular lymphocyte predominant Hodgkin lymphoma, which is classified separately)
• ✓Query provider for anatomic site when available to use a more specific code
• ✓Ann Arbor staging documentation
• ✓Treatment status: active therapy, watch-and-wait, or surveillance
• ✓Provider assessment during the encounter

Commonly Confused Codes