New for FY2027 ICD-10-CM · October 1, 2026
Q87.A: Loeys-Dietz syndrome
By the HCC Buddy Coding Team
The official ICD-10-CM descriptor is Loeys-Dietz syndrome. The FY2027 annual edition starts October 1, 2026. Check the edition that applies to the encounter or inpatient discharge, including any April update.
Billable code. Verified against the official FY2027 order file.
FY2027 Tabular instructions
Instructions below include applicable chapter, section and parent-code notes. Each note identifies where it appears in the official source.
Instructional note
Codes from this chapter are not for use on maternal records
Source: Q00-QA1 (chapter, inherited).
Excludes2
inborn errors of metabolism (E70-E88)
Source: Q00-QA1 (chapter, inherited).
Instructional note
code(s) to identify all associated manifestations
Source: Q87 (category, inherited).
Excludes1
arterial tortuosity syndrome (Q87.82)
Source: Q87.A (self, direct).
Excludes1
Ehlers-Danlos syndrome (Q79.6)
Source: Q87.A (self, direct).
Excludes1
Marfan syndrome (Q87.40-Q87.43)
Source: Q87.A (self, direct).
Excludes1
other systemic involvement of connective tissue (M35)
Source: Q87.A (self, direct).
Compare the FY2027 additions, removals and billable-status changes
What does Q87.A mean in FY2027?
The official ICD-10-CM descriptor is Loeys-Dietz syndrome. The FY2027 annual edition starts October 1, 2026. Check the edition that applies to the encounter or inpatient discharge, including any April update.
When did Q87.A become an ICD-10-CM code?
Q87.A is new for FY2027 ICD-10-CM, effective October 1, 2026. It is absent from the FY2026 April order file. Use the code set that applies to the encounter or inpatient discharge date, and check the official Tabular instructions.
Is Q87.A billable in FY2027?
The FY2027 order file marks Q87.A as billable. Check the complete Tabular instructions and documentation before assigning it.
Does Q87.A map to an HCC?
Q87.A is not in the current CMS mapping file (it is new for FY2027), and CMS has not yet published payment year 2028 mappings. No HCC category or RAF coefficient is shown.
Source: CMS FY2027 ICD-10-CM order file. Payment model: CMS CY 2027 Rate Announcement. Read the FY2027 Official Guidelines.